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Paratesticular rhabdomyosarcoma (PRMS) is a rare and aggressive tumor in children and adolescents.Clinically, it is often revealed by the accidental discovery of a large painless bursa.The therapeutic strategy depends on the stage of the tumor and on the prognostic group according to the Intergroup Rhabdomyosarcoma Study (IRS) classification.We report the case of a patient treated in our institution for a paratesticular rhabdomyosarcoma of the embryonic type discovered at a late stage in an adolescent, with the aim of confirming the fatal evolution of this pathology with “awful” metastatic potential.

The chordoma is a very rare notochordal tumor, the cutaneous localization (chordoma cutis) is even rarer and generally follows a local invasion of the integument even a metastasis. The clinical presentation is non-specific and the diagnosis is often late. It is confirmed by the immunohistochemical characteristics of the tumor. Total surgical excision is necessary in order to avoid the local recurrence which represents a frequent character of this tumor. We report the case of a young patient with perineal chordoma evolving from childhood. To our knowledge, our patient represents the first case of chordoma cutis of the perineum without a history of chordoma.