1. End-stage renal disease in a patient with congenital lymphangiectasia and lymphedema
- Author
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Sombolos, Kostas I., Papachillea, Aristea I., Natse, Taisir M., Gogos, Kostas I., Pavlidis, Georgios O., Barboutis, Kostas A., and Mavromatidis, Kostas S.
- Subjects
Chronic kidney failure -- Case studies ,Chronic kidney failure -- Care and treatment ,Hemodialysis -- Usage ,Lymphedema -- Case studies ,Lymphedema -- Care and treatment - Abstract
Byline: Kostas I. Sombolos (1), Aristea I. Papachillea (1), Taisir M. Natse (1), Kostas I. Gogos (1), Georgios O. Pavlidis (1), Kostas A. Barboutis (1), Kostas S. Mavromatidis (1) Keywords: KeywordsaEnd-stage renal disease; Hemodialysis; Lymphangiectasia; Lymphedema Abstract: Congenital lymphangiectasia with lymphedema is a disorder constituting the main defect in many different genetic syndromes. Herein we describe a 23-year-old male patient with congenital lymphangiectasia and severe lymphedema of the right leg, scrotum, and abdominal wall, who presented with end-stage renal disease, presumably due to cystic renal lymphangiectasia, and is undergoing chronic hemodialysis treatment. Author Affiliation: (1) Renal Unit G.H. "G. Papanikolaou," Thessaloniki, Greece, GR (2) Vas. Olgas 82, 546 43, Thessaloniki, Greece e-mail: sobolos@spark.net.gr Fax: +30-31-829963, GR Article note: Received: 19 April 2000 / Revised: 4 October 2000 / Accepted: 5 October 2000
- Published
- 2001
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