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Byline: J. Snajdauf (1), O. PetrA- (1), K. Pycha (1), M. Rygl (1), J. Kalousova (1), R. Keil (2), R. Kodet (3) Keywords: Porcelain gallbladder; Extrahepatic bile duct obstruction; Long-term biliary stenting Abstract: An extrahepatic bile duct obstruction was diagnosed in a 13-year-old boy presenting with pruritus, abdominal pain and jaundice. Several weeks after sphincterotomy and biliary stenting via endoscopic retrograde cholangiopancreaticography which relieved the obstruction, the patient was operated on. Severe fibrosis encased the extrahepatic biliary tract, so only cholecystectomy was performed because planned hepaticojejunoanastomosis could jeopardize the vascular supply to the liver. Histopathology showed calcification of the gallbladder wall and chronic fibroproliferative changes in the surrounding tissue. The stricture of extrahepatic biliary duct resolved after 3 years of repeated replacement of stents. The stenting was thereafter terminated. In the following 3 years no dilation of intrahepatic bile ducts and no laboratory signs of cholestasis recurred and the now 19-year-old boy is doing well. Neither a case of porcelain gallbladder with extrahepatic bile duct obstruction in a child nor a successful treatment of the obstruction by long-term stenting has been described in the literature yet. Author Affiliation: (1) Department of Paediatric Surgery, 2nd Medical School, Teaching Hospital Motol, Charles University in Prague, V Avalu 84, 150 00, Prague 5, Czech Republic (2) Department of Internal Medicine, 2nd Medical School, Teaching Hospital Motol, Charles University in Prague, V Avalu 84, 150 00, Prague 5, Czech Republic (3) Department of Pathology and Molecular Medicine, 2nd Medical School, Teaching Hospital Motol, Charles University in Prague, V Avalu 84, 150 00, Prague 5, Czech Republic Article History: Registration Date: 11/11/2005 Accepted Date: 27/10/2005 Online Date: 01/12/2005