45 results on '"Zabner, Joseph"'
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2. CYSTIC FIBROSIS: Airway acidification initiates host defense abnormalities in cystic fibrosis mice
3. Starting a Lung Transplant Program: A Roadmap for Long-term Excellence
4. Mitochondrial-Targeted Antioxidant Therapy Decreases Transforming Growth Factor-β-Mediated Collagen Production in a Murine Asthma Model
5. Impaired mucus detachment disrupts mucociliary transport in a piglet model of cystic fibrosis
6. Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs
7. Transepithelial migration of neutrophils into the lung requires TREM-1
8. REDUCED AIRWAY SURFACE PH IMPAIRS BACTERIAL KILLING IN THE PORCINE CF LUNG: S3.3
9. Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung
10. Hoechst increases adeno-associated virus-mediated transgene expression in airway epithelia by inducing the cytomegalovirus promoter
11. Enamel Pathology Resulting from Loss of Function in the Cystic Fibrosis Transmembrane Conductance Regulator in a Porcine Animal Model
12. Do Cell Junction Protein Mutations Cause an Airway Phenotype in Mice or Humans?
13. Concentration of the antibacterial precursor thiocyanate in cystic fibrosis airway secretions
14. Loss of Cystic Fibrosis Transmembrane Conductance Regulator Function Produces Abnormalities in Tracheal Development in Neonatal Pigs and Young Children
15. Role of CFTR on Sinus Development and Disease in the CF Pig
16. PULMONARY INNATE IMMUNITY AND CYSTIC FIBROSIS: S1.3
17. Patterns and density of early tracheal colonization in intensive care unit patients
18. Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs
19. Drosophila are protected from Pseudomonas aeruginosa lethality by transgenic expression of paraoxonase-1
20. Cellular Localization and Activity of Ad-Delivered GFP-CFTR in Airway Epithelial and Tracheal Cells
21. A Novel Host Defense System of Airways Is Defective in Cystic Fibrosis
22. The Coxsackievirus and Adenovirus Receptor: A new adhesion protein in cochlear development
23. TRACHEAL COLONIZATION IN NEWLY INTUBATED PATIENTS
24. The Role of the Extracellular Domain in the Biology of the Coxsackievirus and Adenovirus Receptor
25. Lysozyme Secretion by Submucosal Glands Protects the Airway from Bacterial Infection
26. The CCT Promoter Directs High-Level Transgene Expression in Distal Lung Epithelial Cell Lines
27. Segregation of receptor and ligand regulates activation of epithelial growth factor receptor
28. Histamine Decreases E-Cadherin-Based Adhesion To Increase Permeability of Human Airway Epithelium*
29. Interleukin-9 Induces Goblet Cell Hyperplasia during Repair of Human Airway Epithelia
30. Inflammatory Response in Airway Epithelial Cells Isolated from Patients with Cystic Fibrosis
31. Thixotropic Solutions Enhance Viral-Mediated Gene Transfer to Airway Epithelia
32. Targeting the urokinase plasminogen activator receptor enhances gene transfer to human airway epithelia
33. Increasing Epithelial Junction Permeability Enhances Gene Transfer to Airway Epithelia In Vivo
34. Absence of amiloride-sensitive sodium absorption in the airway of an infant with pseudohypoaldosteronism
35. Feline immunodeficiency virus vectors persistently transduce nondividing airway epithelia and correct the cystic fibrosis defect
36. Activity of Abundant Antimicrobials of the Human Airway
37. Augmentation of Lung Liquid Clearance via Adenovirus-mediated Transfer of a Na,K-ATPase [small beta, Greek]1 Subunit Gene
38. Incorporation of Adenovirus in Calcium Phosphate Precipitates Enhances Gene Transfer to Airway Epithelia In Vitro and In Vivo
39. Comparison of DNA-Lipid Complexes and DNA Alone for Gene Transfer to Cystic Fibrosis Airway Epithelia In Vivo
40. Lack of High Affinity Fiber Receptor Activity Explains the Resistance of Ciliated Airway Epithelia to Adenovirus Infection
41. Adenovirus-Mediated Gene Therapy for Head and Neck Squamous Cell Carcinomas
42. Repeat Administration of an Adenovirus Vector Encoding Cystic Fibrosis Transmembrane Conductance Regulator to the Nasal Epithelium of Patients with Cystic Fibrosis
43. A Mouse Model for the Delta F508 Allele of Cystic Fibrosis
44. Adenoviral-mediated Gene Transfer to Fetal Pulmonary Epithelia In Vitro and In Vivo
45. Normal Sweat Chloride Values Do Not Exclude the Diagnosis of Cystic Fibrosis
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