1. Optical coherence tomography image in gelatinous drop-like corneal dystrophy: case report
- Author
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Isabel Habeyche Cardoso, Otávio de Azevedo Magalhães, Samuel Rymer, Sergio Kwitko, Lucia Maria Kliemann, and Diane Ruschel Marinho
- Subjects
medicine.medical_specialty ,Corneal dystrophies, hereditary ,Tomography, optical coherence ,Corneal dystrophy ,Criança ,Corneal opacity ,Hereditary/diagnosis ,Cornea ,Optical coherence tomography ,lcsh:Ophthalmology ,Ophthalmology ,Case report ,Medicine ,Humans ,Child ,Tomography ,Optical coherence/methods ,Opacidade da córnea ,Relato de caso ,Relatos de casos ,medicine.diagnostic_test ,business.industry ,Distrofias hereditárias da córnea ,Dystrophy ,General Medicine ,medicine.disease ,Humanos ,Tomografia de coerência óptica ,lcsh:RE1-994 ,Corneal dystrophies ,Child, Preschool ,Gelatinous drop-like corneal dystrophy ,Female ,sense organs ,business ,Amyloidosis, Familial - Abstract
A distrofia corneana gelatinosa em gotas é uma desordem rara e pouco descrita em nossa literatura. O caso apresentado demonstra a dificuldade de realizar o diagnóstico nas fases mais iniciais da doença. O uso de modernos exames de imagem, como a tomografia de coerência óptica de segmento anterior, auxilia no diagnóstico e pode ser crucial para definir a melhor conduta terapêutica. Apresentaremos as alterações histopatológicas e as características clínicas desta incomum distrofia. Gelatinous drop-like corneal dystrophy is a rare disorder with few cases described in the present literature. The following report will show how difficult it is to diagnose this disease in early stages. Modern image exams, such as optical coherence tomography helps to diagnose and can be crucial to establish the best treatment. We will present the histopathological changes and clinical features in this unusual dystrophy.