1. Amyloid transthyretin cardiac amyloidosis with different manifestations, test findings and types.
- Author
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Budweg J, Al-Ani M, Assaf Y, Parker A, and Aranda J
- Subjects
- Humans, Prealbumin, Diagnostic Imaging, Electrocardiography, Amyloid Neuropathies, Familial complications, Amyloid Neuropathies, Familial diagnosis, Amyloid Neuropathies, Familial therapy, Heart Failure diagnosis, Heart Failure etiology, Cardiomyopathies diagnosis, Cardiomyopathies therapy
- Abstract
Amyloid transthyretin amyloidosis usually presents with cardiac amyloidosis manifestations, most commonly with a heart failure syndrome. The history and physical examination offer clues of other cardiac and extracardiac manifestations. Taking a detailed history is essential in elucidating pertinent family and medical history that may increase suspicion for amyloidosis. Further, certain findings on electrocardiogram and imaging should raise suspicion and trigger further workup that can confirm the diagnosis, since treatment is evolving., Competing Interests: Competing interests: None declared., (© BMJ Publishing Group Limited 2023. No commercial re-use. See rights and permissions. Published by BMJ.)
- Published
- 2023
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