1. Management of a child with von Willebrand disease (type 2A) and extensive burns: a case report
- Author
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Christophe Magnin, Marc Bertin-Maghit, Laure Fayolle-Pivot, Bernard Allaouchiche, Sylvie Tissot, and Sandrine Meunier
- Subjects
Pediatrics ,medicine.medical_specialty ,Treatment outcome ,Blood Loss, Surgical ,Hemorrhage ,von Willebrand Disease, Type 2 ,Critical Care and Intensive Care Medicine ,Drug Administration Schedule ,Blood loss ,hemic and lymphatic diseases ,von Willebrand Factor ,Von Willebrand disease ,medicine ,Humans ,Severe burn ,Child ,Bleeding episodes ,Burn wound ,business.industry ,Coagulants ,General Medicine ,medicine.disease ,Von Willebrand disease type 2A ,Treatment Outcome ,Coagulation ,Emergency Medicine ,Surgery ,Female ,business ,Burns - Abstract
Von Willebrand disease (VWD) is a common inherited bleeding disorder. Its diagnosis is based on the association of bleeding symptoms and specific biological data [1,2]. The cornerstone of its treatment is the replacement of the deficient protein during acute spontaneous bleeding episodes or before invasive procedures. It may induce haemorrhagic morbidities in severe burn since the coagulation homeostasis is frequently impaired by itself in that setting and since excision and closure of burn wound are regularly required in such patients. However, the specific management of patients with both severe burn and type 2A VWD has not yet been described. We therefore report a paediatric case of type 2A VWD admitted for severe burn.
- Published
- 2011