1. Skin Manifestations, Multiple Aneurysms, and Carotid-Cavernous Fistula in Ehlers-Danlos Syndrome Type IV
- Author
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Joo Sung Kim, Seung-Chyul Hong, Hong Sik Byun, Jay-Hyun Koh, Won Ro Lee, Duk-Kyung Kim, Young Soo Do, and Yeon Hyeon Choe
- Subjects
Adult ,Carotid Artery Diseases ,medicine.medical_specialty ,Contusions ,Ecchymosis ,Physical examination ,EASY BRUISABILITY ,Renal Artery ,Arterio-Arterial Fistula ,Physiology (medical) ,Humans ,Medicine ,Multiple aneurysms ,Ocular pain ,Carotid-cavernous fistula ,Skin manifestations ,medicine.diagnostic_test ,business.industry ,medicine.disease ,Aneurysm ,Ehlers-Danlos syndrome type IV ,Surgery ,Radiography ,Angiography ,Ehlers-Danlos Syndrome ,Female ,Cardiology and Cardiovascular Medicine ,business ,Carotid Artery, Internal - Abstract
A21-year-old woman presented with left ocular pain and severe pulsatile headache. She had suffered from easy bruisability since she was young. On physical examination, ecchymoses and bruises were noticed on trauma sites (Figure 1A⇓). The skin was so thin that subcutaneous blood vessels were visible (Figure 1B⇓). Huge hematomas and ecchymoses occurred at the puncture sites after angiography (Figure 1C⇓). There was no significant hyperelasticity of the skin. …
- Published
- 1999