1. Diffuse panniculitis in a teenage male with ZZ α 1 -antitrypsin deficiency.
- Author
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Papiris SA, Parmaxidis A, Theotokoglou S, Tsakiraki Z, Veith M, Panagiotou A, Pappa V, Kallieri M, Mornex JF, Katoulis AC, Haritos D, Panayiotides IG, and Manali ED
- Abstract
Diffuse panniculitis is a rare manifestation of α
1 -ATD, albeit perhaps the most fulminant and life-threatening complication, associated usually with ZZ phenotype. Intravenous α1 -AT treatment is lifesaving. https://bit.ly/3EDmCzT., Competing Interests: Conflict of interest: S.A. Papiris declares payment or honoraria from DEMO SA, in the 36 months prior to manuscript submission. J-F. Mornex declares consulting fees from CSL Behring, Grifols, LFB and Takeda; and payment or honoraria and support for attending meetings from CSL Behring, Grifols and LFB, all in the 36 months prior to manuscript submission; and that they are a member of the scientific board of ADAAT. E.D. Manali declares support for attending meetings from CSL Behring in the 36 months prior to manuscript submission. All other authors declare no competing interests., (Copyright ©The authors 2023.)- Published
- 2023
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