1. Large monophasic synovial sarcoma of the mediastinum in a 15-year old boy
- Author
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Spiros Loggos, Fotios Mitropoulos, George Oikonomopoulos, and Konstandinos Kondrafouris
- Subjects
Male ,Pulmonary and Respiratory Medicine ,medicine.medical_specialty ,Time Factors ,Adolescent ,Heart Ventricles ,Multiple Organ Failure ,medicine.medical_treatment ,Vena Cava, Inferior ,Case Reports ,Mediastinal Neoplasms ,Inferior vena cava ,Sarcoma, Synovial ,Fatal Outcome ,Monophasic Synovial Sarcoma ,medicine ,Humans ,Neoplasm Invasiveness ,Heart Atria ,Cardiac Surgical Procedures ,Cardiopulmonary Bypass ,business.industry ,Mediastinum ,Plastic Surgery Procedures ,medicine.disease ,Chemotherapy regimen ,Synovial sarcoma ,Mediastinal Neoplasm ,Tumor Burden ,Surgery ,Radiation therapy ,Circulatory Arrest, Deep Hypothermia Induced ,Treatment Outcome ,medicine.anatomical_structure ,medicine.vein ,Disease Progression ,cardiovascular system ,Deep hypothermic circulatory arrest ,Cardiology and Cardiovascular Medicine ,business - Abstract
We present the interesting case of a 15-year old boy with a monophasic synovial sarcoma (MSS) of the mediastinum, which was infiltrating the right heart chambers and the inferior vena cava (IVC). A radical excision was performed, with extensive reconstruction of the heart, under deep hypothermic circulatory arrest. Radical surgical excision is considered to be the treatment of choice for these lesions, as chemotherapy and radiotherapy have little effect. Unfortunately, the patient and his parents refused any further consultation with an oncologist and, although there was no recurrence at 12 months following the procedure, at 24 months we were informed of his death due to the tumour appearing on the left cardiac chambers with subsequent multi-organ failure.
- Published
- 2012
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