1. Expert management of congenital portosystemic shunts and their complicationsKey points
- Author
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Valérie Anne McLin, Stéphanie Franchi-Abella, Timothée Brütsch, Atessa Bahadori, Valeria Casotti, Jean de Ville de Goyet, Grégoire Dumery, Emmanuel Gonzales, Florent Guérin, Sebastien Hascoet, Nigel Heaton, Béatrice Kuhlmann, Frédéric Lador, Virginie Lambert, Paolo Marra, Aurélie Plessier, Alberto Quaglia, Anne-Laure Rougemont, Laurent Savale, Moinak Sen Sarma, Olivier Sitbon, Riccardo Antonio Superina, Hajime Uchida, Mirjam van Albada, Hubert Petrus Johannes van der Doef, Valérie Vilgrain, Julie Wacker, Nitash Zwaveling, Dominique Debray, and Barbara Elisabeth Wildhaber
- Subjects
congenital portosystemic shunt ,pulmonary hypertension ,hepatocellular carcinoma ,adenoma ,focal nodular hyperplasia ,β-catenin ,Diseases of the digestive system. Gastroenterology ,RC799-869 - Abstract
Summary: Congenital portosystemic shunts are often associated with systemic complications, the most challenging of which are liver nodules, pulmonary hypertension, endocrine abnormalities, and neurocognitive dysfunction. In the present paper, we offer expert clinical guidance on the management of liver nodules, pulmonary hypertension, and endocrine abnormalities, and we make recommendations regarding shunt closure and follow-up.
- Published
- 2024
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