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Atrophia maculosa varioliformis cutis (AMVC) is a rare form of idiopathic non-inflammatory macular atrophy that occurs in young individuals.[1] It is characterized by the spontaneous development of depressed lesions on the face arranged in a varioliform, linear or reticulated pattern in the absence of previous trauma or inflammation.[2] A familial occurrence has been reported.[[1], [6]] Its pathogenesis remains unknown, and its exact nosology is still a matter of conjecture. Dermatological examination revealed a bilateral distribution of a few linear, depressed lesions on the cheeks, three punctate, depressed lesions located on the trunk and two on the dorsum of the feet (Fig.). GLO:3NZ/01nov19:jdv15721-fig-0001.jpg PHOTO (COLOR): Upper row: bilateral linear, depressed lesions on the cheeks (left) and chin (right); Lower row: punctate, depressed lesions on the trunk (left) and on a foot (right). gl. [Extracted from the article]

Aplasia cutis congenita (ACC) is a rare malformation characterized by a localized absence of skin. Seventeen cases of classic ACC presented as scarring alopecia oval (4/17) or star-shaper (13/17); 2/17 cases of scarring ACC involved a large area of the scalp (>5 cm) and required a neurosurgical approach. In three children with non-scarring ACC-associated with hair collar sign plus naevus flammeus, we respectively detected: (i) a cranial meningocele, (ii) malformation of the venous system of the occipital area, and (iii) syndactyly and brachydactyly (Adam-Oliver syndrome). [Extracted from the article]