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Introduction: Aortic coarctation is a frequent congenital cardiovascular disorder representing 5–8% of all cases. It is typically localized in the isthmic region. However, in about 1% of cases coarctation may develop in atypical sites of the aorta and it is frequently complicated with severe hypertension. Aim: The aim of the authors was to present diagnostic and surgical methods used in 27 patients with atypical aortic coarctation during the last 35 years with special interest on long-term results. Method: There was a great advance in diagnostic and surgical treatment methods during the time period analyzed in this study. Nowadays morphologic diagnosis is most commonly obtained using computed tomography angiography and magnetic resonance angiography. Some cases were treated with endovascular techniques, but the authors used also a wide variety of surgical approaches in these patients with atypical aortic coarctation. Results: No patient died after surgery and hypertension was reduced in all patients, too. Reintervention was necessary in patients operated in childhood due to change of body measures. Conclusions: Atypical aortic coarctation can be treated surgically with good early and late outcomes. Somatic growth of children may indicate surgical revision. Orv. Hetil., 2016, 157(26), 1043–1051.

Atherosclerosis is a generalized degenerative disease of arteries. A rare manifestation of that is the penetrating atheromatous aortic ulceration of the aortic wall which may be complicated by subintimal hematoma, dissection, false aneurysm and rupture (acute aortic syndrome).The aim of the authors was to analyse their experience with this rare disease.In the department of the authors 10,212 patients underwent surgery for cardiovascular diseases. Among these, 18 patients were diagnosed with penetrating atheromatous aortic ulceration located in the thoracic aorta (ascending aorta 2, aortic arch 8, descending aorta 6 and thoracoabdominal aorta 2 patients). Severe comorbidities were present in the majority of patients.Depending on the localisation the authors used various treatment options such as open surgery (4 patients), hybrid techniques (7 patients) and pure endografting (7 patients). One patient died on postoperative day 3. Two patients had late complications due to endoleaks treated successfully by open surgery.The authors conclude that when this dangerous condition detected in time, a wide variety of open, hybrid and endovascular methods can be applied with good results.Bevezetés: Az arteriosclerosis generalizált érbetegség, de egyes verőérszakaszokon eltérő súlyossággal jelentkezhet. Speciális ritka megjelenési formája az aorta atheromás fekélyképződése, ami hajlamosít subintimalis bevérzésre, dissectióra, álaneurysma-képződésre és rupturára (akut aortaszindróma). Célkitűzés: A szerzők célja a kórkép kezelésével szerzett tapasztalatok ismertetése. Módszer: A szerzők osztályán 10 212, szív-ér rendszeri betegség miatt operált beteg közül 18 esetben találtak penetráló ulcust a thoracalis aorta különböző szakaszain. Az aorta ascendensen, az aortaíven, az aorta descendensen és thoracoabdominalis aortán kialakult elváltozásokat több esetben számos társbetegség súlyosbította. Nyolc beteg tünetekkel, 10 tünetmentes állapotban került felfedezésre. Eredmények: A lokalizációtól függően megválasztott nyitott (n = 4), hibrid (n = 7) és endovascularis (n = 7) beavatkozásokat végeztek. A korai posztoperatív szakban egy beteget veszítettek el. Két betegnél az aneurysmazsák endograft körüli telődése miatt nyitott műtét vált szükségessé, amely után a betegek zavartalanul gyógyultak. Következtetések: A szerzők tapasztalata szerint e veszélyes kórkép időben felfedezve a rendelkezésre álló technikai lehetőségek révén jó eredménnyel kezelhető. Orv. Hetil., 2014, 155(12), 461–468.

Aortic coarctation is a frequent congenital cardiovascular disorder representing 5-8% of all cases. It is typically localized in the isthmic region. However, in about 1% of cases coarctation may develop in atypical sites of the aorta and it is frequently complicated with severe hypertension.The aim of the authors was to present diagnostic and surgical methods used in 27 patients with atypical aortic coarctation during the last 35 years with special interest on long-term results.There was a great advance in diagnostic and surgical treatment methods during the time period analyzed in this study. Nowadays morphologic diagnosis is most commonly obtained using computed tomography angiography and magnetic resonance angiography. Some cases were treated with endovascular techniques, but the authors used also a wide variety of surgical approaches in these patients with atypical aortic coarctation.No patient died after surgery and hypertension was reduced in all patients, too. Reintervention was necessary in patients operated in childhood due to change of body measures.Atypical aortic coarctation can be treated surgically with good early and late outcomes. Somatic growth of children may indicate surgical revision.

The prevalence of congenital aortic coarctation is 4 in 10 000 live birth. Aortic coarctation is typically located in the aortic isthmus, but it may occur at atypical sites. Treatment options include both surgical and endovascular interventions. In patients undergoing surgical or endovascular intervention late complications such as recoarctation or aortic aneurysm may develop.The aim of the authors was to analyse their own experience in late complication and treatment options of aortic coarctation operated in childhood.Retrospective analysis of data of 32 patients treated between 1980 and 2014 for late complications 8-42 years after surgical treatment of aortic coarctation.In 28 patients aneurysm formation after isthmic patch plasty was found. Two patients had aortobronchial fistula, 2 patients showed anastomosis disruption and 2 patients had graft stenosis. During operation hybrid solution was performed in 23 patients, isthmic aorto-aortic inlay graft interposition in 5 patients, aorto-aortic bypass in 2 patients, subclavio-aortic bypass in 2 patients, graft patch plasty in one patient and ilio-renal bypass in one patient. Complications included severe intraoperative bleeding in one patient and pneumothorax in one patient. No early or late mortality occurred.The authors conclude that life long control is mandatory in order to detect late complications in patients who underwent operation of aortic coarctation in childhood.Bevezetés: Az aortacoarctatio előfordulása 10 000 élve született gyermek közül 4 esetben várható. Isthmicus és atípusos, az aorta bármely szakaszán kialakuló változatait ismerjük. Számos sebészi és endovascularis megoldás ismert. Mindkét megoldás után késői szövődmények jelentkezhetnek, mint recoarctatio vagy aneurysmaképződés. Célkitűzés: A szerzők az aortacoarctatio késői szövődményeivel és azok megoldási lehetőségeivel kapcsolatos saját tapasztalatok elemzését tűzték ki célul. Módszer: 32 beteg kórtörténetének retrospektív elemzését végezték, akiknél 1990–2014 között gyermekkorban végzett coarctatioműtét szövődményének ellátására került sor 8–42 évvel a műtét után. Eredmények: 28 esetben a foltplasztika leszakadása okozott álaneurysmát, 2 esetben aortobronchialis fistulát, 2 betegnél anastomosisdisruptiót, 2 esetben graftstenosist. A distalis aortaív hibrid műtétét végezték 23 esetben, aortoaorticus isthmicus graft interpositiót 5 esetben, új aortoaorticus bypasst 2 esetben, új subclavioaorticus bypasst, graftfoltplasztikát és iliorenalis bypasst 1-1 esetben. Egy esetben hárítottak el intraoperatív vérzést és egy betegnél emphysemás bullaruptura miatt kétszer kényszerültek thoracotomiára. Következtetések: A szerzők rendkívül fontosnak tartják a betegek évenkénti ellenőrzését. A késői elváltozások kezelésében egyre inkább a hibrid műtétek kerültek előtérbe, de egyes súlyos esetekben továbbra is nyitott műtét jelentette a megfelelő megoldást. Orv. Hetil., 2014, 155(30), 1189–1195.

This paper deals with a novel chapter of aneurysm surgery, the stent-graft implantation. The interdisciplinary cooperation between angio-radiology and surgery made available a much less invasive therapeutic option. The new technique was first applied in 1991.The authors present the technique, conditions and results of the procedure and also give a survey on the domestic situation.In general anaesthesia using inguinal approach a self-expanding stent-graft (diameter: 8 mm) equipped with barbs was inserted in the aorta and deployed into the aneurysm under X-ray guidance. Vanguard (Boston-Scientific Co.), Talent (Medtronic Co.) and Exluder (Gore-Tex Co.) instruments were used.In 40 patients (29 men and 11 women, mean age: 59.7 years) 55 stent-grafts were implanted. Thirty-one thoracic and 9 infrarenal aneurysms were treated. In 3 patients ruptured aneurysm, in 3 other instances covered ruptured aneurysm, and in 3 persons symptomatic aortic aneurysm were treated. Thirty-one patients underwent elective procedures. Two deaths occurred in the early, and 4 in the late postoperative period (at months 3, 6, 7 and 36 postoperatively). In 9 patients adjunctive vascular surgery interventions were performed in 13 instances. Primary endoleak occurred in 3, whereas secondary endoleak was observed in 4 instances. All of these healed spontaneously. The authors compared the domestic results with internationally published data. This included 1120 traditional aneurysm resections and 110 stent-graft implantations performed in Hungary and 2283 surgical and 3843 endovascular procedures published in international scientific journals.The indications for this new procedure are still being formed. Despite the higher incidence of complications, this less traumatic intervention can be applied with benefit for patients. Nevertheless, at the time being, financial considerations may prevent the more widespread use in the practice. In Hungary the conditions are already available for this endovascular treatment and the authors support its employment.