1. Aphallia: a review to standardize management.
- Author
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Gabler, Tarryn, Charlton, Robyn, Loveland, Jerome, and Mapunda, Ellen
- Subjects
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PENIS abnormalities , *RESUSCITATION , *URINARY diversion , *URETHROPLASTY , *MEDICAL decision making - Abstract
Congenital aphallia is a rare anomaly with little supporting literature and controversial management. The aim of this review is to assess the most recent literature with a focus on staged management of these cases. We performed a PubMed search of all English literature in the past 10 years using the term aphallia. Twenty-three articles were identified of which six were excluded. A further three papers meeting our criteria were found in the references to papers initially identified. We found that management can be staged in three phases: short, intermediate and long-term. We conclude that optimal short-term management centers on resuscitation and urinary diversion as necessary, intermediate-term management entails urethrorectal fistula division, urethrostomy and neophallus creation and long-term management results in successful neophalloplasty, urethroplasty, prosthetic implant and continued protection of the upper urinary tracts with a Mitrofanoff. All this within a multidisciplinary team ensuring shared decision-making with the patient and their family. [ABSTRACT FROM AUTHOR]
- Published
- 2018
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