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Sclerosing encapsulating peritonitis is a very rare pathological entity. It is a chronic fibroinflammatory disease affecting the peritoneum and leading to the formation of diffuse egg-shell-shaped fibrous capsule which totally or locally encapsulate the abdominal viscera, in particular the digestive tract. Clinical signs are little specific and misleading. Medical imaging, including computed tomography, can help clinicians to make a diagnosis, by highlighting a thin peritoneal membrane encompassing an agglutination of digestive loops. Secondary types (postperitoneal dialysis, tuberculosis, medications, postintraperitoneal chemotherapy) are quite common, however idiopathic sclerosing encapsulating peritonitis is very rare and few cases have been reported in the literature. We here report the case of a 53-year-old woman with idiopathic sclerosing encapsulating peritonitis., Competing Interests: Les auteurs ne déclarent aucun conflit d'intérêts, (Copyright: Nizar El Bouardi et al.)

Emergency diagnosis of small bowel volvulus can be established in patients with acute intestinal obstruction, or even shock, or repeated abdominal pain often associated with motility disorders. This is a life-threatening complication of common incomplete mesentery, which is defined as an intestinal malrotation occurring very rarely in adults. Clinical symptoms are non-specific, hence the importance of knowing the radiological features, in particular scannographic features of this rare entity, thus enabling early therapeutic management. We here report the case of a 65-year-old patient admitted with total small bowel volvulus complicating common incomplete mesentery, diagnosed based on abdominal computed tomography (CT) scan and confirmed at surgery, who had favorable outcome., Competing Interests: Les auteurs ne déclarent aucun conflit d´intérêts., (Copyright: Amina Alaoui et al.)

Gayet Wernicke encephalopathy (EGW) is a neurological emergency secondary to thiamine deficiency (vitamin B1). This is more often secondary to chronic alcoholism. The purpose of this study is to remind clinicians of some clinical signs different from ethylism, suggesting EGW as well as to report four cases characterized by different types of anomalies shown by MRI. The average age of patients was 40 years (2 females 2 males). The neurological picture was characterized by disorders of vigilance in all patients, oculomotor disorders in 2 cases, and cerebellar ataxia in one patient. Chronic vomiting was reported in two cases, prolonged fasting in the first case and alcoholism in the second case. MRI of the brain showed anomalies suggesting EGW in all patients with contrast enhancement in one case. Thiamin deficiency was confirmed in two patients. In our context EGW seems to be more frequent in pathological circumstances other than chronic alcoholism (chronic vomiting, severe malnutrition, severe starvation, and chemotherapy...). The clinical signs can suggest other pathologies such as cerebral venous thrombosis, stroke, or other metabolic disorders but MRI excluded them and allowed the diagnosis of EGW. MRI of the brain has an essential role in the diagnosis of EGW. Absence or delay in treatment may influence the prognosis., Competing Interests: Les auteurs ne déclarent aucun conflit d´intérêts., (Copyright: Siham Bouchal et al.)

We report the case of a 28 year old young man with congenital diaphragmatic hernia, detected at a later stage due to occlusive syndrome manifesting on the scanner as small intestine and colonic distension upstream of a strangulated Bochdalek's diaphragmatic hernia. The patient underwent laparotomy with reduction of the hernia and closure of the diaphragmatic rupture. This study aims to update the current understanding of a rare cause of intestinal obstruction, strangulated Bochdalek's diaphragmatic hernia, whose diagnosis is essentially based on radiological examinations based on the scanner data, which allows early management., Competing Interests: Les auteurs ne déclarent aucun conflit d'intérêts., (© Mustapha Iken et al.)

Jejunal pseudoaneurysm is a rare complication of pancreatitis, usually manifested by digestive bleeding when it ruptures into the digestive lumen. This complication is extremely rare and may be life-threatening. The diagnosis is based on abdominal angiographic computed tomography. Radiology allows therapeutic management through arterial embolization. This case report describes a pseudoaneurysm of jejunal artery that developed as the result of pancreatitis: A 77-year-old man seen in early September 2015 at the emergency department for acute pancreatitis had a pseudocyst infected and spontaneously fistulized into the jejunum lumen. His condition responded initially to symptomatic therapy, and he was discharged. He returned two years later, with digestive bleeding from jejunal pseudoaneurysm that had ruptured into the jejunal lumen. Angiographic embolization was performed as first-line treatment with good outcome. Bleeding more than two years after acute pancreatitis due to rupture of a jejunal pseudoaneurysm is an exceptional complication. Here we report a rare case of digestive hemorrhage caused by jejunal pseudoaneurysm, complicating acute pancreatitis., (Copyright © 2019 Elsevier Masson SAS. All rights reserved.)

We here report a case of multiple gastrointestinal stromal tumors (GIST) in the small bowel detected in a patient with peritonitis. The peculiarity of this case study is the intraoperative detection of multifocal small bowel tumor masses, suggesting gastrointestinal stromal tumors on postoperative CT scan. Tumor couldn't be suspected clinically on the basis of peritonitis., Competing Interests: Les auteurs ne déclarent aucun conflit d’intérêts.

Creutzfeldt-jakob disease (CJD) is a very rare and fatal disease affecting the central nervous system. It is characterized by mental deterioration leading to progressive dementia, pyramidal and extrapyramidal symptoms as well as myoclonus. Early diagnosis is essential to prevent human-to-human transmission. We here report the case of a 62-year old patient in whom the diagnosis of sporadic CJD was retained based on his clinical status including dementia-related deterioration with myoclonus preceded by behavioral disorders, hallucinations and depression and on brain MRI data showing hyperintensities at the level of the striatum and the cortex on FLAIR and diffusion-weighted imaging sequences., Competing Interests: Les auteurs ne déclarent aucun conflit d'intérêts.

Anti-synthetase syndrome (ASS) is an inflammatory myopathy commonly associated with pulmonary involvement, especially parenchymal (diffuse infiltrative pneumonitis). Extrathoracic manifestations associated with pulmonary involvement can give an indication to the diagnosis: myalgias, polyarthralgias, Raynaud's syndrome, erythematous palmar hyperkeratosis with fissures and fever. Given the suggestive clinical and radiological picture, the presence of aminoacyl-transfer RNA (tRNA) synthetase antibodies enables to confirm, in particular, Anti Jo-1 antibody activity. Pulmonary involvement is a major prognostic factor, hence the indication for intensive immunosuppressive therapy based on corticosteroids, immunosuppressive medications or the association among them. A better awareness about this disorder revealed by pulmonary manifestations could enable early and adequate management and to improve patient's prognosis., Competing Interests: Les auteurs ne déclarent aucun conflit d´intérêts.

We report a case of Sturge-Weber-Krabbe Syndrome diagnosed in the Department of Radiology at the Hassan II University Hospital in Fes. This study highlights the clinical diagnostic and therapeutic features as well as the evolutionary characteristics of this uncommon neuroradiologic disorder., Competing Interests: Les auteurs ne déclarent aucun conflit d’intérêts.