1. [Cardiac pseudotumor revealing Behçet's disease]
- Author
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C, Darie, M, Knezinsky, S, Demolombe-Rague, L, Pinède, M, Périnetti, J F, Ninet, and J, Ninet
- Subjects
Adult ,Heart Diseases ,Behcet Syndrome ,Humans ,Female ,Thrombosis - Abstract
Cardiac thrombosis is a rare complication of Behçet's disease (BD), which may present as a cardiac tumor. Its discovery precedes, in half of the cases, the diagnosis of BD. The high mortality may be associated to postsurgical complications and/or an associated involvement of pulmonary arteries.We present the case of a 31 years old Caucasian French woman, with a history of venous thromboembolic disease, who had surgery after the discovery of a right ventricle tumor. That was an organised thrombus with endomyocardial fibrosis and a diagnosis of Behçet's disease was made after the surgery. The outcome was favourable under medical treatment associating corticosteroids, colchicine and antivitamin K (AVK), without relapse four years later.The discovery of an intracardiac mass in a young patient must evoke the diagnosis of cardiac thrombus and Behçet's disease, even in the absence of predisposing ethnic or geographic factor.
- Published
- 2004