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Additional file 1: Supplementary Methods. Fig. S1. Ophthalmologic findings of the ALSP patient with AARS1 mutation. Fig. S2. Aminoacylation and misaminoacylation kinetics assays of AlaRS T606I. Table S1. Clinical, imaging and pathological characteristics of CSF1R, AARS2 and AARS1-related diseases. Table S2. Phenotype-genotype correlation in AARS1-related diseases.

With the continuous development of the level of economy and the continuous improvement of the level of science and technology, the continuous enrichment of household appliances has led to a decrease in the load factor of the grid and a large difference between the peaks and valleys, which affects the safety and stability of the power grid. This paper introduces the concepts of WiFi technology, smart home and demand response, as well as its development status and trends. Then, this paper designs a smart home power management system based on the theory of WiFi technology and demand response. In this paper, the overall structure of the system, the hardware design and the software design are explained. Through this system, users can achieve an energy-efficient and efficient living environment and better participate in the demand response.