1. Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries.
- Author
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Jin JB, Robinson JD, Camarda JA, Satzer MB, Carr MR, Monge M, and Patel A
- Subjects
- Infant, Newborn, Male, Humans, Pulmonary Artery diagnostic imaging, Tricuspid Atresia diagnostic imaging, Tricuspid Atresia surgery, Pulmonary Valve diagnostic imaging, Pulmonary Valve abnormalities, Heart Defects, Congenital surgery, Pulmonary Atresia diagnostic imaging, Pulmonary Atresia surgery, Ventricular Septum
- Abstract
Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically significantly dilated. We present the case of a newborn male prenatally diagnosed APV-TA with intact ventricular septum (IVS) and nearly discontinuous branch pulmonary arteries, the surgical strategy employed, and the salient hemodynamic factors considered in the medical decision-making., (© 2023. The Author(s), under exclusive licence to Springer Science+Business Media, LLC, part of Springer Nature.)
- Published
- 2024
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