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Maffucci's syndrome is manifested by multiple enchondromatoses and hemoangioma in the same individual. A case of Maffucci's syndrome in a sixty-one-year-old woman who elected to have a hemipelvectomy, because her left pubis have changed chondrosarcoma, is reported.A brief review of literature reveals that twenty-five cases of Maffucci's syndrome, including our case have been reported in Japan.It is said to have no sex predilection, but male: 9, female: 15, unknown 1, in my collection and that in three cases of these sarcomatous degeneration occurred, giving a malignancy rate of twelve per cent.

Two cases of pathological fracture of the femur from metastatic tumor were reported, which were treated with bone cement. The method is indicated not only for the severely affected pathological fracture of long bones but also for the prophylactic operation.

21-year-old man was admitted to the Department of Orthopaedic Surgery, Kyushu University with a 3 year old history of pain and bulging out of the sternum. A marked balooned out cystic lesions of the corpus sterni was demonstrated. Giant cell tumor Type II was confirmed on histological examination.After en bloc resection of the corpus sterni including both II, III, IV costosternal joints and lower part of manubrium. Three pieces of big iliac grafts were fixed to cover the defect as reconstruction operation.Six months postoperatively, roentgenograms were satisfactory with evidence of bony barrier formation. The patient's course continued to be satisfactory.