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Ocular lens defects and inner ear type hearing loss are seen individually in juveniles quite frequently. Concomitance of these abnormalities or association with other anomalies is attested to by the multiplicity of syndromes, diseases, and symptom complexes which have been described. Juvenile renal disease associated with hearing loss or ocular disease has also been reported, 1-7 but the combination of simultaneous chronic renal disease, inner ear hearing loss, and lens abnormality is infrequent. Goldbloom and associates 8,9 described the clinical findings in a boy with chronic nephritis who developed bilateral nerve deafness at 11 years of age and later was noted to have "an unusual type of bilateral anterior subcapsular cataract." Two brothers, one of whom had inner ear hearing loss, died of chronic renal disease, and the mother had chronic nephritis. Although this was postulated to have been an inherited characteristic, an investigation of four generations of the family

Displacements of the lens can be classified into three groups, namely, congenital, traumatic, and spontaneous (or consecutive). In nearly all of the cases in these types the primary disturbance is in the lens zonule, which is the most important structure in maintaining the position of the lens. In the congenital group there is a failure of development of the normal anatomic relations of the lens zonule and the lens may become displaced before birth or in postnatal life, even several decades after birth. In the traumatic type of displacement there is an actual tearing, directly or indirectly, of the zonules. The spontaneous type results from some ocular disorder, such as uveal inflammation, high myopia, hydrophthalmos, or hypermature cataract. The mechanism involved here consists of zonular or vitreal degeneration with subsequent displacement of the lens. Traction bands pulling the lens out of position have been previously observed. These have developed following