1. Currarino triad: A case report of a 48-year-old patient with a neuroendocrine tumor
- Author
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Teresa Vilares, Joao Rebelo, Roberto Silva, Nuno Silva, Rui Cunha, Ana I Marques, and António J. Madureira
- Subjects
lcsh:Medical physics. Medical radiology. Nuclear medicine ,medicine.medical_specialty ,Chronic constipation ,Gastrointestinal ,business.industry ,lcsh:R895-920 ,Currarino triad ,Sacral Agenesis ,030218 nuclear medicine & medical imaging ,03 medical and health sciences ,Triad (sociology) ,0302 clinical medicine ,Anal imperforation ,Neuroendocrine tumor ,Male patient ,Sacral agenesis ,medicine ,Rare syndrome ,Presacral mass ,Radiology, Nuclear Medicine and imaging ,Radiology ,business ,030217 neurology & neurosurgery ,ANAL IMPERFORATION - Abstract
Currarino triad is a rare syndrome, with less than 250 cases reported, and it includes a combination of sacrococcigeal bony abnormalities, anorectal malformations and the presence of a presacral mass. Here we present a case of a 48-year-old male patient with history of severe chronic constipation, who was incidentally diagnosed with a presacral during imagiological investigation, which was histologically proven to be a neurendocrine tumor.
- Published
- 2020