Search

Patient initials or identifier number N/A ### Relevant clinical history and physical exam Degos Disease, also known as malignant atrophic papulosis, is a very rare, genetic disease with an unclear etiology. It is a distinctive vasculopathy syndrome characterized by a thrombotic diathesis

A five-membered radiographic constellation is characteristic of S.L.E.: (1) minimal bilateral fibrinous pleuritis; (2) ill-defined patches or linear bands or plaques in the lung bases; (3) fluctuation in the size and configuration of the heart; (4) slight enlargement of the spleen; (5) conspicuous lack of irreversible structural damage to the joints. The first four can be seen frequently on serial chest roentgenograms. Table IV is a statistical summary of these findings. IV . Organ or tissue involved Usual manifestation Per cent of patients found positive Pleura Pleuritis 74 Lung Pneumonitis 50 Heart Carditis 53 Spleen Slight enlargement 34 Joint Minimal osteoporosis 26