1. Characteristics and outcomes of the Spanish registry for pediatric patients with bicuspid aortic valve (REVAB).
- Author
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Juzga-Corrales C, Ayerza-Casas A, Figueras-Coll M, Escribà-Bori S, Plata-Izquierdo B, Collell R, González-Marín MA, Siurana JM, Sorlí M, Albert de la Torre L, Teodoro-Marín S, Rodríguez M, Domínguez-García O, Rellán S, Manso B, López-Abel B, Álvarez-Pérez R, Portillo-Márquez M, Rezola E, Centeno-Malfaz F, Solana-Gracia R, Rojo-Sombrero H, Cantero-Tejedor MT, Riaño B, Tejero-Hernández MÁ, Jiménez-Casso M, Pérez-Pardo AM, Moriano-Gutiérrez A, Marrero-Calvo M, Fernández MT, Salido-Peracaula C, Bravo MJ, Gutiérrez-Larraya F, and Sabaté-Rotés A
- Subjects
- Male, Humans, Child, Aortic Valve, Retrospective Studies, Registries, Bicuspid Aortic Valve Disease complications, Bicuspid Aortic Valve Disease pathology, Heart Valve Diseases epidemiology, Heart Valve Diseases pathology, Heart Defects, Congenital epidemiology, Heart Defects, Congenital complications, Aortic Valve Stenosis complications
- Abstract
Introduction and Objectives: Bicuspid aortic valve (BAV) disorder is the most common congenital heart disease. The aim of this study was to describe the characteristics of 0- to 18-year olds with BAV in a population-based registry., Methods: Data from all pediatric patients were obtained from the Spanish registry for pediatric patients with bicuspid aortic valve (REVAB) (< 18 years). For data analysis, patients with BAV were divided into 2 groups by their features: isolated BAV and BAV with associated congenital heart disease., Results: We included 1681 patients from 33 hospitals. Males accounted for 69.6% (n = 1158). Valve morphology was horizontal in 63.4% (n = 1012) and pure (Sievers type 0) in 28.4% (n=469). Isolated BAV was present in 63.7% (n=1060), and concomitant left-sided obstructive lesions in 23.4% (n=390). Interventions were required in 8.6% (n=145)., Conclusion: These data represent the first large, population-based description of the clinical presentations and outcomes of patients enrolled in the Spanish registry for pediatric patients with bicuspid aortic valve., (Copyright © 2023. Published by Elsevier España, S.L.U.)
- Published
- 2023
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