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6 results on '"Pulmonary Alveolar Proteinosis complications"'

1. Pulmonary Alveolar Proteinosis in Association with Secondary Hemophagocytic Lymphohistiocytosis.

Author

Lin J, De A, Figueiredo L, Maxwell R, Wasserman E, Adams K, Weingarten J, Peek G, and Miksa M

Subjects
Abnormalities, Multiple diagnosis, Abnormalities, Multiple therapy, Biopsy, Needle, Combined Modality Therapy, Female, Follow-Up Studies, Humans, Immunohistochemistry, Infant, Lymphohistiocytosis, Hemophagocytic complications, Pulmonary Alveolar Proteinosis complications, Radiography, Thoracic methods, Rare Diseases, Respiration, Artificial, Respiratory Insufficiency diagnosis, Respiratory Insufficiency etiology, Respiratory Insufficiency therapy, Risk Assessment, Severity of Illness Index, Tomography, X-Ray Computed methods, Tracheostomy methods, Treatment Outcome, Lymphohistiocytosis, Hemophagocytic diagnosis, Lymphohistiocytosis, Hemophagocytic therapy, Pulmonary Alveolar Proteinosis diagnosis, Pulmonary Alveolar Proteinosis therapy
Abstract

Pulmonary alveolar proteinosis (PAP) is a rare diffuse lung disease in the pediatric population. There are currently few cases documenting hemophagocytic lymphohistiocytosis as a cause for secondary PAP. We describe an ex-preterm child with secondary hemophagocytic lymphohistiocytosis, complicated by PAP and hypoxemic respiratory failure., (Copyright © 2016 Elsevier Inc. All rights reserved.)

Published
2017
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2. Recurrent fatal pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance.

Author

Santamaria F, Brancaccio G, Parenti G, Francalanci P, Squitieri C, Sebastio G, Dionisi-Vici C, D'argenio P, Andria G, and Parisi F

Subjects
Amino Acid Transport Disorders, Inborn urine, Fatal Outcome, Humans, Infant, Lysine urine, Male, Recurrence, Amino Acid Transport Disorders, Inborn complications, Heart-Lung Transplantation, Pulmonary Alveolar Proteinosis complications, Pulmonary Alveolar Proteinosis surgery
Abstract

We present a case of recurrent pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance. The recurrence of the pulmonary disease provides further insight regarding the possible pathogenesis of pulmonary alveolar proteinosis and therapeutic options for this complication.

Published
2004
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3. Inherited surfactant protein-B deficiency.

Author

Hamvas A

Subjects
Animals, Disease Models, Animal, Humans, Infant, Newborn, Lung Diseases complications, Lung Diseases diagnosis, Lung Diseases genetics, Lung Diseases pathology, Lung Diseases therapy, Lung Transplantation, Metabolism, Inborn Errors complications, Metabolism, Inborn Errors diagnosis, Metabolism, Inborn Errors pathology, Metabolism, Inborn Errors therapy, Mice, Proteolipids genetics, Pulmonary Alveolar Proteinosis complications, Pulmonary Surfactants genetics, Lung Diseases metabolism, Metabolism, Inborn Errors genetics, Proteolipids metabolism, Pulmonary Surfactants metabolism
Published
1997

4. Critical illness neuromuscular disease in children manifested as ventilatory dependence.

Author

Sheth RD, Pryse-Phillips WE, Riggs JE, and Bodensteiner JB

Subjects
Adolescent, Asthma complications, Child, Critical Illness, Female, Humans, Male, Meningococcal Infections complications, Neuromuscular Diseases etiology, Pulmonary Alveolar Proteinosis complications, Respiratory Insufficiency etiology, Shock, Septic complications, Syndrome, Ventilator Weaning, Neuromuscular Diseases diagnosis, Respiratory Insufficiency diagnosis, Ventilators, Mechanical
Abstract

Four children with prolonged dependency on a ventilator were found to have reversible quadriparesis, muscle wasting, and hyporeflexia after 8 to 20 days of assisted ventilation for life-threatening sepsis or respiratory failure. Critical illness neuromuscular disease, which was recently recognized as a distinct clinical syndrome in adults, may also be manifested in children by prolonged ventilatory dependency.

Published
1995
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5. Combination of membrane oxygenator support and pulmonary lavage for acute respiratory failure.

Author

Cooper JD, Duffin J, Glynn MF, Nelems JM, Teasdale S, Scott AA, and Martin B

Subjects
Adult, Busulfan adverse effects, Female, Humans, Leukemia, Myeloid complications, Leukemia, Myeloid therapy, Oxygenators, Membrane, Pulmonary Alveolar Proteinosis complications, Pulmonary Fibrosis chemically induced, Lung, Perfusion, Pulmonary Alveolar Proteinosis therapy, Respiratory Insufficiency therapy, Therapeutic Irrigation
Abstract

A 24-year-old woman with chronic granulocytic leukemia and alveolar proteinosis required extracorporeal membrane oxygenator support for respiratory failure refractory to conventional therapy. During perfusion, each lung was lavaged with 10 L. of normal saline. The lavage led to marked clearing of the lungs and improvement in pulmonary function. Extracorporeal support was terminated successfully after 54 hours. The patient died 2 weeks later with bone marrow insufficiency and overwhelming sepsis. Pulmonary lavage is technically feasible during venovenous oxygenator bypass, and may be of value, since such lavage debrides alveoli as well as the bronchial tree. Because pulmonary lavage provides a possible means of improving pulmonary function, it seems worthy of consideration as an adjunct to membrane oxygenator support.

Published
1976

6. Pulmonary alveolar proteinosis and pulmonary cryptococcosis in an adolescent boy.

Author

Sunderland WA, Campbell RA, and Edwards MJ

Subjects
Adolescent, Amphotericin B therapeutic use, Biopsy, Catheterization, Cryptococcosis drug therapy, Humans, Lipids analysis, Lung pathology, Lung Diseases, Fungal complications, Lung Diseases, Fungal drug therapy, Male, Proteins analysis, Pulmonary Alveolar Proteinosis diagnostic imaging, Pulmonary Alveolar Proteinosis metabolism, Pulmonary Alveolar Proteinosis pathology, Pulmonary Alveolar Proteinosis therapy, Radiography, Sex Factors, Therapeutic Irrigation, Vital Capacity, Cryptococcosis complications, Lung Diseases, Fungal microbiology, Pulmonary Alveolar Proteinosis complications
Published
1972
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