1. Treatment of Hepatic Embryonal Undifferentiated Sarcoma With Cardiothoracic Involvement
- Author
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José A. Montero-Argudo, Carlos Domínguez-Massa, Fernando Hornero-Sos, Óscar R Blanco-Herrera, Alberto Berbel-Bonillo, and Félix Serrano-Martínez
- Subjects
medicine.medical_specialty ,Liver tumor ,medicine.medical_treatment ,030204 cardiovascular system & hematology ,Inferior vena cava ,law.invention ,Heart Neoplasms ,03 medical and health sciences ,0302 clinical medicine ,law ,Cardiopulmonary bypass ,Humans ,Medicine ,Heart Atria ,Cardiac Surgical Procedures ,Child ,Endarterectomy ,Cardiopulmonary Bypass ,business.industry ,Liver Neoplasms ,Cancer ,Sarcoma ,General Medicine ,Hypothermia ,medicine.disease ,Magnetic Resonance Imaging ,Right pulmonary artery ,Surgery ,030228 respiratory system ,medicine.vein ,Echocardiography ,Pediatrics, Perinatology and Child Health ,Circulatory system ,Female ,medicine.symptom ,Tomography, X-Ray Computed ,Cardiology and Cardiovascular Medicine ,business - Abstract
Thorough study is required to decide the appropriate management of hepatic tumors in children. We present a case report of a hepatic embryonal undifferentiated sarcoma with unfavorable prognosis in a nine-year-old girl. After undergoing a detailed cancer characteristics and extension study, a two-stage surgery approach was decided. The hepatic tumor resection was the first procedure to be performed. One week later, under cardiopulmonary bypass, deep hypothermia, and circulatory arrest, thrombectomy of the inferior vena cava and right atrium was accomplished, plus thromboendarterectomy of the right pulmonary artery. During a four-year follow-up, the patient continues to be disease-free.
- Published
- 2018
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