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Key Clinical Message We report a compound heterozygous mutation (c.135delC; c.423+2dupT) of MLC1 gene in a Chinese patient underlying infantile macrocephaly and neurological deterioration in early childhood. Brain MRI revealed diffusion abnormality in swollen white matter and a subcortical cyst. The cDNA sequencing analysis for the c.423+2dupT variant revealed skipping of exon 5. [ABSTRACT FROM AUTHOR]

Retinitis pigmentosa (RP) prevalence data in Asia were limited and mainly reported in previous studies of single ethnicity (Xu et al. 2006; Sen et al. 2008; Sharon & Banin 2015). The six eyes with early-stage RP had pigmentary changes at the mid-periphery region, modestly attenuated arterioles without bone-spicule deposits (Fig. The remaining six eyes with mid-stage RP had bone-spicule deposits at the mid-peripheral retina, involving at least two quadrants of retina (Fig. [Extracted from the article]

Strain rate sensitivity will change the cyclic mechanical response of materials under multiaxial thermomechanical fatigue loading; thus, it will lead to errors in fatigue life prediction if strain rate sensitivity is not considered in constitutive simulation. In order to more accurately express the time/rate dependence of viscoplastic behavior, a strain rate sensitivity factor is proposed to modify the viscoplastic function of Chaboche model first. On this basis, a viscoplastic constitutive model considering strain rate sensitivity under multiaxial thermomechanical fatigue loading is proposed, which can describe the varying influence of strain rate sensitivity on cyclic mechanical behavior. Meanwhile, the exponential isotropic hardening rule with the linear term is adopted to characterize the initial rapid softening and subsequent stable softening of the material under fatigue loading at elevated temperature. Moreover, the material‐dependent nonproportional hardening coefficient and the loading path‐dependent rotation factor are used in the kinematic hardening rule to consider the effect of nonproportional additional hardening on the cyclic mechanical behavior of materials. Finally, the proposed method is verified by the stress–strain data of titanium alloy TC4 and Ni‐based superalloy GH4169 under uniaxial and multiaxial thermomechanical fatigue loadings, and a good agreement is obtained. HighlightsThe time/rate dependence of viscoplastic behavior is expressed more accurately.Initial rapid cyclic softening and subsequent stable cyclic softening are described.The effect of nonproportional hardening on cyclic mechanical behavior is considered.The proposed model is verified by two materials with different damage types. [ABSTRACT FROM AUTHOR]

The new compound NH4{ [Zn4(DACH)7(H2O)3] [VIII3VIV18P6 O60(DACH)3]}·19H2O (DACH: 1,2-diaminocyclohexane) is synthesized by hydrothermal reaction of NH4VO3, Zn(OAc)2, DACH, H3PO4, and H2O (autoclave, 160 °C, 6 d). [ABSTRACT FROM AUTHOR]

Antenna arrays that incorporate MIMO technology for indoor–outdoor network interconnection on the same terminal, i.e., for DCS 1800, PCS 1900, WCDMA, 3G, 802.11a/b/g, Bluetooth®, ZigBee®, WiMAX™, and UWB standards, are proposed. Staircase profile printed circuit antennas, monopoles (PCM), and slots (PCS) with VSWR < 2 bandwidth mainly from 1.12 to 10.1 GHz are previously designed, simulated, constructed, and measured as antenna elements for those arrays. For comparison, prototypes for two-element PCM and PCS MIMO arrays have been constructed and measured. The choice should be made according to the directivity required by the final application and portable device size. For the worst signal interference case, the operational bandwidth ranges from 1.5 to 9.9 GHz and from 1.7 to 11.4 GHz for the PCM and the PCS MIMO arrays, respectively. VSWR is basically below two, average capacity loss 0.32 bps/Hz with respect to the ideal uncorrelated (2,2) case and envelope correlation lower than 20 dB. © 2010 Wiley Periodicals, Inc. Microwave Opt Technol Lett 52:889–895, 2010; Published online in Wiley InterScience (www.interscience.wiley.com). DOI 10.1002/mop.25047 [ABSTRACT FROM AUTHOR]