24 results on '"Malek, Abdolreza"'
Search Results
2. Coronavirus disease 2019-related Kawasaki syndrome: a case report
- Author
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Aelami, Mohammad Hasan, Malek, Abdolreza, and Saeidinia, Amin
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- 2022
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3. Rapidly progressing pediatric Lupus with Diffuse Alveolar Hemorrhage and CNS involvement.
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Vahedi, Mahdieh, Nejad Shahrokh Abadi, Reza, Malek, Abdolreza, Toosi, Farrokh Seilanian, Naseri, Maryam, and Hashemi, Narges
- Subjects
SYSTEMIC lupus erythematosus ,LOSS of consciousness ,HEMORRHAGE ,COUGH ,PROGNOSIS ,AUTOIMMUNE diseases - Abstract
Key Clinical Message: Systemic Lupus Erythematosus (SLE) can have an insidious onset and a fatal prognosis in children. Patients presenting without typical signs of SLE should undergo further evaluation if they are not responding to the initial diagnosis and treatment. This is especially true for patients with rapidly progressing symptoms and deterioration in spite of treatment. Pediatric Systemic Lupus Erythematosus is a chronic autoimmune disorder with various organ involvement pulmonary involvement in the course of this disorder is a rare yet potentially life‐threatening complication. In this case report we highlight the findings of a 16‐year‐old girl acutely and initially presenting with cough and fever, eventually complicating to diffuse alveolar hemorrhage and gradual loss of consciousness. Although the patient was started on immunosuppressive treatment after the diagnosis of lupus, based on renal and hematological impairment, was made and initially responded, she eventually deteriorated. [ABSTRACT FROM AUTHOR]
- Published
- 2024
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- View/download PDF
4. Genetic and Clinical Study of Children with Familial Mediterranean Fever in Northeastern Iran
- Author
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Malek, Abdolreza, primary, Abbaszadegan, Mohammadreza, additional, Vakili, Niloofar, additional, Zeraati, Tina, additional, Ghayoor Karimiani, Ehsan, additional, and Sadrnabavi, Arian, additional
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- 2024
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5. Clinical Findings of Sydenham Chorea in Pediatric Patients: A Single-Center Retrospective Study
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Shahri, Hassan Mottaghi Mohaddam, primary, Nejad, Ehsan Hassan, additional, Toosi, Mehran Beiraghi, additional, Malek, Abdolreza, additional, and Payandeh, Asma, additional
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- 2023
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6. Bilateral expansion of mandible and maxillae in a 5‐year‐old girl
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Movahedi, Nasim, primary, Malek, Abdolreza, additional, and Ziaee, Vahid, additional
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- 2022
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7. A Case Report of Renal Tubular Acidosis Type 1 without Glomerular Disease in an Adolescent with Pediatric-onset Systemic Lupus Erythematosus.
- Author
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Malek, Abdolreza, Seyedkaboli, Sepideh, Batouri, Asma, khuban, Amir Muhammad, and Vahedi, Mahdieh
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RENAL tubular transport disorders , *SYSTEMIC lupus erythematosus , *KIDNEY glomerulus diseases , *LUPUS nephritis , *ACIDOSIS , *KIDNEY stones , *TEENAGE girls - Abstract
Introduction: Between 50-75% of children and adolescents with systemic lupus erythematosus (SLE) experience kidney involvement within the first year of diagnosis. The gold standard for diagnosing renal involvement in SLE is a renal biopsy. It is uncommon for SLE to cause isolated tubular involvement without any glomerular disease. Case Presentation: We report an adolescent girl with a known history of systemic lupus erythematosus who presented to the emergency department with progressively worsening weakness. The diagnosis revealed that she had distal renal tubular acidosis (RTA) without any glomerular disease. Her history of nephrocalcinosis and kidney stones on renal ultrasound is most consistent with distal renal tubular acidosis diagnosis. Conclusion: This case highlights the importance of considering renal tubular acidosis lupus patients who experience recurrent hypokalemic episodes. When a patient presents with a normal anion gap metabolic acidosis and hyperchloremia, without evidence of gastrointestinal HCO3 loss or absorption of exogenous acid, renal tubular acidosis (RTA) should be considered. [ABSTRACT FROM AUTHOR]
- Published
- 2023
8. Cardiac Tamponade: A Rare Manifestation of Familial Mediterranean Fever
- Author
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Malek, Abdolreza, Zeraati, Tina, Sadr-Nabavi, Ariane, Vakili, Niloofar, and Abbaszadegan, Mohammad Reza
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Article Subject - Abstract
Familial Mediterranean fever (FMF) typically presents with recurrent attacks of fever and serosal inflammation with peritoneum, pleura, and synovium. We usually do not expect pericardial involvement at the early stages. FMF is an autoinflammatory disease, usually inherited with an autosomal recessive pattern. The patients typically have biallelic mutations in the MEFV gene, located on chromosome 16. Colchicine is the first-line treatment of FMF, which not only plays a crucial prophylactic role regarding the attack episodes, but also prevents amyloidosis. Colchicine resistance and intolerance in FMF patients have been rarely reported. Alternative anti-inflammatory agents are understood to be helpful in such cases. We describe a 13-year-old boy referred to our pediatric department complaining of chest pain, dyspnea, and tachycardia. Due to the massive pericardial and pleural effusion, a pericardiocentesis was performed, and a chest tube was inserted. Cardiac tamponade was considered as the initial diagnosis. After a month, he faced another episode of pleuritic chest pain, fever, tachycardia, and pleural and pericardial effusion. Evaluation for probable differential diagnoses including infection, malignancy, and collagen vascular disease showed no remarkable results. Finally, the mutation found by whole exome sequencing was confirmed by direct Sanger sequencing revealing a heterozygote c.44G > C (p.Glu148Gln) mutation in exon 2, confirming the clinical diagnosis of familial Mediterranean fever. Since he seemed to be nonresponsive to the maximum standard dose of colchicine, 100 mg of daily dapsone was added to his treatment regimen, which controlled the attack episodes well. FMF, while rarely initiated with cardiac manifestation, should be considered in patients with any early signs and symptoms of cardiovascular involvement.
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- 2022
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9. The Negative Predictive Value of Harada Scoring for Coronary Artery Dilatation or Aneurysm in Children with Kawasaki Disease: A Cross-sectional Study.
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Malek, Abdolreza, Ghodsi, Alireza, and Hamedi, Abdolkarim
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ANEURYSM diagnosis , *CORONARY heart disease risk factors , *ANEURYSMS , *PREDICTIVE tests , *PATHOLOGICAL anatomy , *MANN Whitney U Test , *FISHER exact test , *CORONARY disease , *RISK assessment , *T-test (Statistics) , *CHI-squared test , *MUCOCUTANEOUS lymph node syndrome , *CORONARY arteries , *SENSITIVITY & specificity (Statistics) , *DISEASE risk factors , *DISEASE complications , *CHILDREN - Abstract
Background: The most common cause of coronary artery aneurysms in children is Kawasaki disease (KD). One of the risk ratings used to predict coronary artery aneurysms is the Harada score. This study aims to assess the negative predictive value (NPV) of Harada scoring in children with KD. Methods: This cross-sectional study was conducted in Mashhad (Iran) from January 2014 to December 2017. The Harada score was generated for each patient using demographic, laboratory, and echocardiography data retrieved from their medical records. The patients were divided into typical and atypical cases, and the sensitivity, specificity, positive predictive value (PPV), and NPV were calculated. The Chi square test, independent t test, Mann--Whitney U test, and Fisher exact test were used to analyze the data in SPSS software (version 23.0). P≤0.05 was considered statistically significant. Results: The study involved 168 individuals with a mean age of 29.91±19.52 months, including 103 typical and 65 atypical cases. Regarding cardiac complications, the atypical group had a significantly greater rate of coronary artery tapering (P=0.030). Out of 101 patients with cardiac complications, the Harada score was positive in 57 cases, while it was falsely negative in the remaining 44 patients. The calculated sensitivity, specificity, PPV, and NPV were 56.44%, 53.73%, 64.77%, and 45%, respectively. Conclusion: The findings revealed that the Harada scoring is ineffective in detecting coronary artery aneurysms or dilation in KD patients. [ABSTRACT FROM AUTHOR]
- Published
- 2022
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10. Hip Surgery in Quiescent or Active Tubercular Hip Arthritis; Is Reactivation Risk Really a Matter
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Parsa, Ali, Mirzaie, Maryam, Ebrahimzadeh, Mohammad H., Birjandinejad, Ali, Malek, Abdolreza, and Mousavian, Alireza
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lcsh:RD701-811 ,Hip ,lcsh:Orthopedic surgery ,Active ,Tuberculosis ,Surgery ,Current Concepts Review ,Quiescent ,Reactivation - Abstract
About 15 % of all musculoskeletal tuberculosis (TB) have hip involvement. Early anti-tubercular drug therapy and other conservative treatment including short-term traction and mobilization programs could prevent hip joint destruction. Reactivation of TB accounts for a significant of active TB incidence, especially in the developed countries with a low TB prevalence. The risk of TB activation for population with the latent form of disease is about 5-10%. According to the existing literature surgery in tubercular hip arthritis would be safe once sufficient debridement and precise anti tubercular chemotherapy has been done.
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- 2018
11. COVID-19 Associated Multisystem Inflammatory Syndrome: A Systematic Review and Meta-analysis
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Baradaran, Ashkan, primary, Malek, Abdolreza, additional, Moazzen, Nasrin, additional, and Abbasi Shaye, Zahra, additional
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- 2020
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12. Chronic Recurrent Multifocal Osteomyelitis in a 9-year-old Boy
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Malek, Abdolreza, Aelami, Mohammadhassan, Afzali, Narges, Parsa, Ali, and Jalalinia, Havva
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Bone pain ,lcsh:RD701-811 ,lcsh:Orthopedic surgery ,Chronic multifocal osteomyelitis (CRMO) ,Case Report ,Children - Abstract
Chronic recurrent multifocal osteomyelitis (CRMO) is a rare aseptic, auto-inflammatory bone disorder. CRMO presents with bone pain with or without fever. The diagnosis of CRMO is a diagnosis of exclusion and should be included in the differential diagnosis of chronic inflammatory bone lesions in children. Cultures of the bone are typically sterile, antibiotic therapy does not result in clinical improvement whereas anti-inflammatory drugs improve the condition. Furthermore, biopsy should be considered in chronic and relapsing bone pain and swelling unresponsive to treatment. Herein, we present a nine-year-old boy complaining of recurrent pain in his upper and lower extremities. On examination he had mild fever and cervical lymphadenopathy. He also had experienced bone pain and weight loss in the recent month. Based on biopsy and bone scan he was finally diagnosed with CRMO. Naproxen and Pamidronate was prescribed and he was getting better and returned to normal life and activity without need to corticosteroids.
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- 2017
13. Comparison of Clinical Symptoms and Cardiac Lesions in Children with Typical and Atypical Kawasaki Disease
- Author
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Behmadi, Maryam, primary, Alizadeh, Behzad, additional, and Malek, Abdolreza, additional
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- 2019
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14. Brucella Endocarditis Along with Leukocytoclastic Vasculitis in a Child: A Case Report
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Malek, Abdolreza, primary, Rakhshanizadeh, Forough, additional, and Sasan, Mohammad Saeed, additional
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- 2018
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15. Infantile Systemic Hyalinosis: Report of 17-year Experience
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Raeeskarami, Seyed Reza, Aghighi, Yahya, Afshin, Azadeh, Malek, Abdolreza, Zamani, Ali, and Ziaee, Vahid
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Joint Contractures ,Blond Hair ,Skin Thickness ,Case Report ,Infantile Systemic Hyalinosis ,Hyaline Deposits - Abstract
Background: Infantile Systemic Hyalinosis (ISH) is a very rare autosomal recessive disorder characterized by connective tissue involvement as hyaline deposition in skin, gastrointestinal tract, muscles, glands and other organs. Cases Presentation: We report eight Iranian children (4 male and 4 female) with ISH referred to our hospital from 1996 to 2013. The illness had been diagnosed by clinical manifestations and disease progression. Six of them died and two are alive but very sick. Conclusion: ISH is a very rare disorder with poor prognosis. Seventy five percent of our 8 patients died before 2 years old due to severe diarrhea, malabsorption and/or infection.
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- 2014
16. Erythema Nodosum, the First Clinical Manifestation of Crohn's Disease in a-14 Year-Old Boy: A Case Report.
- Author
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Kianifar, Sheila, Malek, Abdolreza, Kiani, Mohammad Ali, and Goldouzi, Hamid Reza
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CROHN'S disease , *ERYTHEMA nodosum , *SYMPTOMS , *RHEUMATISM , *ADIPOSE tissues - Abstract
Erythema nodosum (EN) is a condition in which the skin suffers from oval-shaped and tender erythematous patches, mostly on the anterior region of the leg and sometimes other parts of the body, including the arms and affects subcutaneous adipose tissue. These patches are self-limiting and usually heal on their own within one to two weeks. This is a case report of a patient who is a 14-year-old boy complained of ovalshaped tender erythematous lesions on the legs of both legs and referred and was hospitalized 5 days ago. The patient continued to complain of pain in both thighs when standing and sitting. The patient developed a high fever upon admission. There was no history of the disease while we were taking his history. All laboratory tests were performed and rheumatic diseases and possible malignancies were evaluated and rejected. The patient was treated with the anti-naproxen, an inflammatory drug, and then the patient's pain and fever decreased. However, the patient suffered from multiple ulcerative lesions in the mouth on the final day of hospitalization. Infectious counseling was performed and he was discharged with a diagnosis of EN in the context of oral herpes. Two days after discharge, the patient suffered from hematochezia. Consequently, he was hospitalized and underwent colonoscopy, which showed multiple mucosal lesions in the esophagus and duodenum, and a sample was sent for pathology. The test result showed Crohn's disease, and the patient was treated immediately. [ABSTRACT FROM AUTHOR]
- Published
- 2021
17. Cervicofacial Emphysema and Pneumomediastinum Following Dental Extraction: Case Report
- Author
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Afzali, Nargess, Malek, Abdolreza, and Attar, Amir Hossein Hashemi
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Dental Extraction ,Pneumomediastinum ,Case Report ,Oral Surgery ,Subcutaneous Emphysema ,respiratory tract diseases - Abstract
Background Pneumomediastinum is commonly caused by iatrogenic injury such as surgery on the cervical planes and chest or by tracheostomy. It is also well known that emphysema may occur after dental treatments using an air turbine drill, but there have been few cases of emphysema which extended to the mediastinum. Case Presentation A 16-year-old boy is presented with subcutaneous emphysema and pneumomediastinum which developed 24 hours after surgery for extraction of an inferior second molar. We first describe history, clinical presentation and radiologic appearance of our patient and then review the literature about oral surgery causing pneumomediastinum. Conclusion Surgical procedures in oral cavity can lead to the development of emphysema and pneumomediastinum when air turbine dental drills are used. To avoid these complications, air turbine high speed drills should be used only in necessary cases.
- Published
- 2011
18. Autosomal Recessive Agammaglobulinemia in Juvenile Idiopathic Arthritis: A Case Report.
- Author
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Feizabadi, Azadeh Zare, Malek, Abdolreza, and Ahanchian, Hamid
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JUVENILE idiopathic arthritis , *AGAMMAGLOBULINEMIA , *MACROPHAGE activation syndrome , *IMMUNOLOGICAL deficiency syndromes , *MOTHERS , *B cells , *GROIN - Abstract
The B lymphocyte developmental blocks agammaglobulinemia, leading to peripheral B cell depletion and plasma immunoglobulin reduction. Agammaglobulinemia is a rare yet severe disease since it is presented with recurrent sinopulmonary and skin, central nervous system, bone, and joint infections. The onset of the disease is reported to be at the age of six months. Associations have been reported between arthritis and immunodeficiency disorders, such as agammaglobulinemia and common variable immunodeficiency (CVID). This study aimed to present the case of a 3.5-year-old female with a three-month history of the swelling of the left knee, mimicking oligoarticular juvenile idiopathic arthritis. After the initiation of immunosuppressive treatment, the patient developed large, tender, erythematous lesions on the inguinal region bilaterally, which developed to ecthyma gangrenosum due to Pseudomonas. The patient's mother also reported recurrent episodes of infections since the patient was a one-year-old infant. Subsequent to the immunological examinations and laboratory tests, the patient was diagnosed with autosomal recessive agammaglobulinemia due to low serum immunoglobulin concentration and the absence of peripheral B cells. Primary immunodeficiency conditions (particularly agammaglobulinemia) and CVID should be considered in children with arthritis and recurrent infections. Moreover, immunological analysis should be performed prior to treatment in these children. [ABSTRACT FROM AUTHOR]
- Published
- 2020
19. Protective role of HLA-DRB1*11 against juvenile idiopathic arthritis living in North Eastern Iran.
- Author
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Rezaieyazdi, Zahra, Kochakzadeh, Morteza, Hatef, Mohammad Reza, Esmaily, Habibollah, Malek, Abdolreza, Valizadeh, Narges, Tabaei, Samira, and Rafatpanah, Houshang
- Subjects
JUVENILE idiopathic arthritis ,PUBLIC health ,ALLELES ,HLA histocompatibility antigens ,POLYMERASE chain reaction - Abstract
Objective(s): Juvenile idiopathic arthritis (JIA) is one of the most common chronic rheumatic diseases in children. The complex nature of this immune-mediated disease owes itself to several predisposing genes and environmental factors affecting its pathogenesis. Conducted in Iran, this study was originally intended to investigate every possible association between HLA DRB1 alleles and a susceptibility to JIA. Materials and Methods: In this case-control study, 45 patients with a definite diagnosis of JIA based on International League against Rheumatism (ILAR) criteria were compared against 46 healthy controls. DNA samples taken from both groups were analyzed using PCR-sequence specific primers (PCR-SSP) method. Data analysis including parametric and nonparametric test and multivariate analysis was undertaken using the SPSS 11.5 software. A P-value< 0.05 was regarded as statistically significant. Results: Mean ages in case group and healthy controls were 14.64±6.21 and 13.73±6.39, respectively with no significant difference between the two groups (P=0.515). Sex difference between JIA group and healthy controls was also not significant (P=0.068) .The frequency of HLA-DRB1*01 was found the most frequent HLA-RB1 in our patients (33.3%). No significant statistical correlation between various HLA-DRB1 alleles and clinical subtypes of the disease could be established from the data. HLA-DRB1*11 was shown to raise protection to JIA (P=0.035, OR=2.755, 95% CI=0.963-8.055) in northeastern Iran. In addition, we found that HLA-RB1*09 is nominally associated with an increased risk of JIA (P=0.56, OR=2, 05, 95% CI=0.18-23.63). Conclusion: HLA-DRB1*11 was shown to raise protection to JIA in northeastern Iran. The disparity of findings in other ethnicities prompts further investigations with larger sample sizes. [ABSTRACT FROM AUTHOR]
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- 2018
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20. Churg-Strauss Syndrome in a Seven-year-old Boy: A Case Report.
- Author
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Malek, Abdolreza, Rakhshanizadeh, Forough, and Kiyanifa, Sheila
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CHURG-Strauss syndrome , *VASCULITIS , *METHOTREXATE - Abstract
Churg-Strauss syndrome (CSS) is a type of vasculitis of small-to-medium sized vessels. This syndrome is known by a history of bronchial asthma with systemic necrotizing vasculitis and peripheral blood hypereosinophilia. It is currently called eosinophilic granulomatosis with polyangiitis (EGPA). This disease affects both genders and all age groups, but it is very rare among children. CSS diagnosis is based on clinical findings such as asthma, eosinophilia, rhinosinusitis, and signs of vasculitis in major organs. In cases where steroids alone or in combination with other immunosuppressive agents are used as treatment, the outcome and long-term survival are usually satisfying. In comparison with other types of systemic vasculitis, the mortality rate of this syndrome is low. In this study, we present the case of a 7-yearold boy with poorly controlled bronchial asthma since three years of age. This case had developed purpuric skin lesions, sinusitis, arthritis, and weakness of the limbs with symptoms of mononeuritis multiplex at the age of seven. After being admitted to our hospital, a series of studies, including complete blood count-diff, chest X-ray, paranasal sinus radiography, brain magnetic resonance imaging, nerve conduction study, spirometry, and serological tests for autoantibodies, were performed and he was diagnosed with CSS. Thereafter, he received regular corticosteroid therapy in combination with methotrexate, and his symptoms were generally well-controlled with the beginning of the treatment. The clinical characteristics, diagnosis, and management of CSS in children are also reviewed in this study. [ABSTRACT FROM AUTHOR]
- Published
- 2018
21. Juvenile Idiopathic Arthritis Onset in a Neonate: A Rare Case Report.
- Author
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Malek, Abdolreza, Sasan, Mohammad-Saeed, Afzali, Narges, Ghahremani, Somayeh, and Ghahremani, Sara
- Subjects
- *
JUVENILE idiopathic arthritis , *RHEUMATOLOGY - Abstract
Background: A common type of chronic arthritis in children and adolescents is juvenile idiopathic arthritis (JIA). According to the International League of Associations for Rheumatology (ILAR) classification, JIA diagnostic criteria include age under 16 years and disease duration of six-weeks. Based on the number of involved joints in the first sixmonths of disease onset, JIA is categorized into oligoarticular or polyarticular subtypes. Age is a characteristic factor in the diagnosis of disease subsets; it is worth mentioning that cases younger than six months of age are seldom found in any of the subtypes. Case report: In this report, we present a rare case of JIA in an infant, presenting at 20 days of age. Effusion of the right hip joint was one of the primary manifestations of the disease. During hospitalization, she went through sepsis workup and a four-week antibiotic therapy for management of lower limb pseudoparalysis. In spite of antibiotic therapy, she developed effusion of a second joint. According to the course and duration of symptoms and ILAR classification for JIA, oligoarticular JIA was diagnosed and treated. Conclusion: In this case, infectious diseases, such as tuberculosis and brucellosis, and malignancies were ruled out as a cause of inflammation through bone marrow aspiration, culture, and tests; ultrasound and magnetic resonance imaging showed no lytic and sclerotic lesions or a fracture. Our experience showed a rare case of JIA and suggested that JIA must be considered in children with joint inflammation at any age. [ABSTRACT FROM AUTHOR]
- Published
- 2017
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22. Abductor digiti minimi opponensplasty for a patient with Cavanagh's syndrome: A case report.
- Author
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Parsa, Ali, Kashani, Farzad Omidi, Moghaddam, Mohammad Hallaj, Malek, Abdolreza, and Birjandinejad, Ali
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EYE movements ,ABDUCTOR pollicis longus muscle - Abstract
Thumb hypoplasia only in the intrinsic thenar muscles is a rare condition; this defect might be accompanied with cardiac diseases (Holt-Oram syndrome), ocular anomalies, and vascular anomalies of the hand and wrist (Okihiro syndrome). In addition, this condition may be detected in hypereosinophilic syndrome (HES), which gives rise to other hand anomalies, as well. Unilateral or bilateral absence of isolated thenar muscles is another rare abnormality. In this study, we presented a case of Cavanagh's syndrome in an eight-year-old boy with right-sided thenar hypoplasia who had difficulty in thumb opposition. For the treatment, the patient underwent abductor digiti minimi (ADM) opponensplasty. After three years of follow-up, he regained thumb opposition and was symptom-free. Care must be taken to avoid misdiagnosis of thenar atrophy/hypoplasia with carpal tunnel syndrome in case of children. [ABSTRACT FROM AUTHOR]
- Published
- 2018
23. Epidemiologic investigation of juvenile rheumatoid arthritis: a ten-year study.
- Author
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Malek, Abdolreza, Aghighi, Yahya, Parvisy, Behnam, Reza Raeeskarami, Seyed, and Ziaee, Vahid
- Subjects
- *
JUVENILE idiopathic arthritis , *RHEUMATISM in children , *RHEUMATOLOGY , *SEX factors in disease , *JOINT diseases - Abstract
Background: Juvenile Rheumatoid Arthritis (JRA) is the most common chronic pediatric rheumatologic disease. There is a wide range of variation in disease subgroup distribution and evolution according to different populations, environments and genetic predisposition. This study was designed to evaluate epidemiologic characteristics of JRA in Iran. Methods: A cross-sectional studies was performed on children suffering from JRA according to American College of Rheumatology during 10 year (2002-2011). Patients' data was recorded in hospital questionnaires; Patients' age at the first presentation and time of diagnosis, sex, ethnicity, early clinical and constitutional presentations, joint involvement pattern and presence of associated diseases were evaluated. Results: In this study, 171 children (91 boys and 80 girls) were enrolled. The mean age of patients was 5.2±3.5 years at the time of presentation and 5.7±3.6 years when the diagnosis was confirmed. The most common type of disease was polyarticular arthritis (41.9%). The prevalence of pauciarticular and systemic onset subtype were 31.6% and 19.3%, respectively. According to ethnicity, the most common incidence was seen in Fars and Turk populations respectively. The most common constitutional presentation was fever. Fever and morning stiffness was significantly higher in polyarticular patients. Extra articular manifestation was seen in 40.4% patients. Among extra-articular manifestations, skin involvement was seen more than others. There was no correlation between sex and type of chronic arthritis. Uveitis was detected in 5.8% of our cases. The mean age was significantly higher in polyarticular group (6.04 year) in comparison to pauciarticular and systemic group (4.4 year in both groups) (P=0.005). There was no correlation between sex and type of chronic arthritis. Conclusion: The prevalence of JRA subgroups was different in Iran comparing with western countries and polyarticular disease was the most common subgroup in this study. Uveitis was less common in this study in comparison to studies in other countries. There is no sex predilection in each subgroup of JRA. [ABSTRACT FROM AUTHOR]
- Published
- 2014
24. Pneumothorax after Mechanical Ventilation in Newborns.
- Author
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Malek, Abdolreza, Afzali, Nargess, Meshkat, Mojtaba, and Yazdi, Nadieh Hosseini
- Subjects
- *
ARTIFICIAL respiration , *COMPUTER software , *NEONATAL intensive care , *PNEUMOTHORAX , *PULMONARY surfactant , *REGRESSION analysis , *DATA analysis , *NEONATAL intensive care units , *CROSS-sectional method - Abstract
Objective: Air leak syndromes including pneumothorax, pneumomediastinum and pulmonary interstitial emphysema are frequent in neonatal period. Mechanical ventilation with positive pressure is one of the most common causes of these syndromes. The aim of this study was to evaluate predisposing factors and incidence of pneumothorax in newborns under mechanical ventilation. Methods: This descriptive cross sectional study was performed in 400 newborns under mechanical ventilation in intensive care unit of a teaching hospital in Iran from April 2004 to December 2008. Predisposing factors leading to ventilation and incidence of air leak syndromes were studied. Sex, gestational age, birth weight, type of delivery, history of surfactant replacement therapy, ventilator settings and mortality rate were recorded. Statistical analysis was done using SPSS software. Univariate analysis and regression analysis were considered. Findings: Among 400 patients under mechanical ventilation, 102 neonates developed pneumothorax (26%). Fifty six (54.9%) of them were boys and 46 (45.1%) girls. 54.9% of newborns with pneumothorax were preterm and 45.1% term. Birth weight less than 2500g was recorded in 59.8%. Fifty two percent of these neonates were born by cesarean section vs. 32% of newborns without pneumothorax. The most common type (62.7%) of ventilation leading to pneumothorax was InspiratoryPositive Pressure Ventilation (IPPV). Surfactant replacement: therapy was recorded In 32^^W cases with pneumothorax compared to 60.4% irfneonatos under ventilation without pneumothorax, which was significantly different (P= 0.017). Conclusion: In newborns surfactant replacement therapy can reduce the risk of pneumothorax caused by mechanical ventilatiö|t. [ABSTRACT FROM AUTHOR]
- Published
- 2011
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