1. Acute coronary syndrome in a patient with Marfan syndrome following emergent surgical repair of aortic dissection.
- Author
-
Bovolato FE, Isabella G, Rampazzo D, Guglielmi C, Gerosa G, Iliceto S, and Bilato C
- Subjects
- Acute Coronary Syndrome, Adult, Angioplasty, Coronary Angiography, Female, Humans, Postoperative Complications, Stents, Aortic Dissection surgery, Aortic Aneurysm surgery, Marfan Syndrome complications
- Abstract
We report a case of acute coronary syndrome in a patient with suspect Marfan syndrome, 25 days after emergent modified Bentall-De Bono intervention for acute type I peripartum aortic dissection. She was admitted to our intensive care unit because of unstable angina, caused by critical blood flow reduction in a large portion of the myocardium, according to the severity of the symptoms and the electrocardiographic alterations. Coronary angiography showed a sub-occlusive stenosis of the left main coronary artery as a result of the dissection extension to the coronary ostium. Because of the high risk related to heart surgery, the patient was successfully treated by unprotected angioplasty and drug-eluting stent positioning. Short- and mid-term outcomes were favourable. Subsequent tests confirmed the diagnosis of Marfan syndrome. After 2 years of follow-up, the patient remains asymptomatic and in good health. To our knowledge, this is the first report of a successful percutaneous intervention of the left main coronary artery in a patient with Marfan syndrome who had already undergone ascending aortic root and valve replacement by the Bentall-De Bono procedure for acute dissection.
- Published
- 2008
- Full Text
- View/download PDF