1. Severe diffuse hypoplasia of the aorta associated with multiple vascular abnormalities
- Author
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Oto Ađić, Slobodan Grebeldinger, and Svetlana S Balj
- Subjects
medicine.medical_specialty ,Adolescent ,Vascular Malformations ,Aorta, Thoracic ,Vascular anomaly ,Celiac Artery ,Mesenteric Artery, Superior ,Internal medicine ,medicine.artery ,medicine ,Humans ,Radiology, Nuclear Medicine and imaging ,Superior mesenteric artery ,Aorta, Abdominal ,Aorta ,business.industry ,Abdominal aorta ,Vascular malformation ,General Medicine ,Aortic bifurcation ,medicine.disease ,Hypoplasia ,Blood pressure ,medicine.anatomical_structure ,Hypertension ,Cardiology ,Surgery ,Female ,Cardiology and Cardiovascular Medicine ,business - Abstract
Hypoplasia of the thoracic and abdominal aorta is an extremely rare vascular pathology. The most common clinical manifestation is severe uncontrolled hypertension in adolescents and young adults. Medical treatment alone can decrease blood pressure, but often very high doses of antihypertensive drugs are needed. When hypertension is refractory to the antihypertensive medications, surgical revascularization is considered as the treatment of choice. We report the case of a severe and diffuse hypoplasia of the aorta, beginning with the aortic isthmus, to the aortic bifurcation, associated with an aberrant celiac trunk and superior mesenteric artery, and with other multiple vascular abnormalities. Unlikely, the only manifestation of this extensive vascular malformation was medicamentously controllable hypertension. To our knowledge, this severe vascular anomaly, with such a minimal clinical manifestation, has not been previously described in the English literature.
- Published
- 2011