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Your search keyword '"Zinna, Shairbanu"' showing total 2 results
Start Over Author "Zinna, Shairbanu" Topic ataxia telangiectasia
2 results on '"Zinna, Shairbanu"'

1. Ataxia telangiectasia: why should the ERS care?

Author

Bhatt JM, Bush A, van Gerven M, Nissenkorn A, Renke M, Yarlett L, Taylor M, Tonia T, Warris A, Zielen S, Zinna S, and Merkus PJ

Subjects
Cough, Deglutition Disorders etiology, Deglutition Disorders physiopathology, Europe, Humans, Immunologic Deficiency Syndromes etiology, Immunologic Deficiency Syndromes immunology, Lung Diseases etiology, Lung Diseases physiopathology, Lung Diseases, Interstitial etiology, Neurodegenerative Diseases etiology, Neurodegenerative Diseases physiopathology, Pneumonia etiology, Pneumonia immunology, Pulmonary Medicine, Recurrence, Respiratory Tract Infections etiology, Respiratory Tract Infections immunology, Sinusitis etiology, Sinusitis immunology, Societies, Medical, Ataxia Telangiectasia complications, Ataxia Telangiectasia immunology
Published
2015
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2. ERS statement on the multidisciplinary respiratory management of ataxia telangiectasia.

Author

Bhatt JM, Bush A, van Gerven M, Nissenkorn A, Renke M, Yarlett L, Taylor M, Tonia T, Warris A, Zielen S, Zinna S, and Merkus PJ

Subjects
Ataxia Telangiectasia diagnosis, Ataxia Telangiectasia genetics, Ataxia Telangiectasia immunology, Ataxia Telangiectasia mortality, Ataxia Telangiectasia physiopathology, Combined Modality Therapy, Comorbidity, Cooperative Behavior, Genetic Predisposition to Disease, Humans, Interdisciplinary Communication, Lung Diseases diagnosis, Lung Diseases genetics, Lung Diseases immunology, Lung Diseases mortality, Lung Diseases physiopathology, Predictive Value of Tests, Risk Factors, Spirometry standards, Tomography, X-Ray Computed standards, Treatment Outcome, Ataxia Telangiectasia therapy, Lung immunology, Lung pathology, Lung physiopathology, Lung Diseases therapy, Patient Care Team standards, Pulmonary Medicine standards
Abstract

Ataxia telangiectasia (A-T) is a rare, progressive, multisystem disease that has a large number of complex and diverse manifestations which vary with age. Patients with A-T die prematurely with the leading causes of death being respiratory diseases and cancer. Respiratory manifestations include immune dysfunction leading to recurrent upper and lower respiratory infections; aspiration resulting from dysfunctional swallowing due to neurodegenerative deficits; inefficient cough; and interstitial lung disease/pulmonary fibrosis. Malnutrition is a significant comorbidity. The increased radiosensitivity and increased risk of cancer should be borne in mind when requesting radiological investigations. Aggressive proactive monitoring and treatment of these various aspects of lung disease under multidisciplinary expertise in the experience of national multidisciplinary clinics internationally forms the basis of this statement on the management of lung disease in A-T. Neurological management is outwith the scope of this document., (Copyright ©ERS 2015.)

Published
2015
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