1. Orbital masses in ANCA-associated vasculitis: an unsolved challenge?
- Author
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Berti, Alvise and Kronbichler, Andreas
- Subjects
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AUTOIMMUNE disease diagnosis , *IMMUNOSUPPRESSIVE agents , *RITUXIMAB , *CYCLOPHOSPHAMIDE , *ADRENOCORTICAL hormones , *AUTOIMMUNE diseases , *BLINDNESS , *DIAGNOSIS , *ORBITAL diseases , *MEDICAL errors , *SERIAL publications , *VASCULITIS , *TREATMENT effectiveness , *SYMPTOMS , *THERAPEUTICS - Abstract
The authors discuss a report on the description of clinical features and disease course of orbital masses in ANCA-associated vasculitis (AAV). Topics discussed include factors predicting the onset of orbital masses in the context of AAV, a diagnostic pathway to minimize diagnostic delay and improve the management of subset of patients, and comparison of first-line treatment of a cyclophosphamide- to a rituximab-based regimen.
- Published
- 2019
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