1. Sturge–Weber Syndrome: Roots to a Cure a Nightmare in Pediatric Dentistry
- Author
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Pooja N Mapara, Savita Hadakar, Sachin Gugawad, Swapnil Taur, Dhanshri Shashikant Khade, Namrata Gaonkar, and Shashikiran N Devendrappa
- Subjects
Tranexamic acid ,Pediatric dentistry ,business.industry ,Sturge–Weber syndrome ,Dentistry ,Case Report ,Orthodontics ,medicine.disease ,Oral cavity ,Dental management ,Computed tomography head ,Port-wine stains ,Nightmare ,Gingival enlargement ,Pediatric patient ,Pediatrics, Perinatology and Child Health ,medicine ,Periodontics ,Clinical significance ,Birthmark ,Oral Surgery ,medicine.symptom ,business ,GNAQ gene ,Congenital disorder - Abstract
Aim and objective This article aims to report a case of Sturge-Weber syndrome (SWS) in a pediatric patient and its systematic dental management to add to the existing literature. Background Sturge-Weber syndrome is one of the vascular disorders, known for its stupendous scope of clinical manifestations and life-threatening complications. The substantial prevalence of oral manifestations in SWS makes it crucial to have a comprehensive knowledge of this rare congenital disorder. Case description This case report represents a case of SWS in an 11-year-old boy with oral, ocular, and neurological features who reported due to pain, unilateral gingival enlargement associated with spontaneous bleeding in the mandibular left region. A multidisciplinary team approach having comprehensive knowledge regarding such rare congenital disorder is a must to prevent its life-threatening complications. Conclusion Sturge-Weber syndrome often affects the oral cavity through vascular lesions. Hence, deep knowledge is immensely important to provide an appropriate dental treatment without complications. Clinical significance Port-wine stains should not be considered as just birthmarks and should be further investigated for its systemic involvement to arrive at a confirmatory diagnosis and treated accordingly with special precautions. How to cite this article Mapara PN, Taur SM, Hadakar SG, et al. Sturge-Weber Syndrome: Roots to a Cure a Nightmare in Pediatric Dentistry. Int J Clin Pediatr Dent 2021;14(1):145-148.
- Published
- 2021
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