1. Unilateral persistent fetal vasculature coexisting with anterior segment dysgenesia.
- Author
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Cañizares B, Yago I, Piñero Á, and Ruiz M
- Subjects
- 22q11 Deletion Syndrome, Abnormalities, Multiple genetics, Anterior Eye Segment diagnostic imaging, Anterior Eye Segment surgery, Corneal Opacity diagnostic imaging, Corneal Opacity etiology, Corneal Opacity genetics, Corneal Opacity surgery, Eye Abnormalities diagnostic imaging, Eye Abnormalities genetics, Eye Abnormalities surgery, Female, Glaucoma, Open-Angle etiology, Humans, Infant, Newborn, Keratoplasty, Penetrating, Persistent Hyperplastic Primary Vitreous diagnostic imaging, Persistent Hyperplastic Primary Vitreous genetics, Persistent Hyperplastic Primary Vitreous surgery, Postoperative Complications etiology, Vitrectomy, Abnormalities, Multiple surgery, Amblyopia etiology, Anterior Eye Segment abnormalities, Corneal Opacity complications, Esotropia etiology, Eye Abnormalities complications, Persistent Hyperplastic Primary Vitreous complications
- Abstract
Case Report: A case is presented of a 4 week-old female neonate with Peters anomaly (PA) and unilateral persistent foetal vasculature (PFV) referred to our centre due to esotropia. At 12 weeks of age, a penetrating keratoplasty and vitrectomy were performed without major complications in the immediate post-operative period. The patient is currently under an intensive treatment for amblyopia and secondary glaucoma., Discussion: Surgical treatment of PFV is controversial, with prevention of amblyopia, phthisis, and glaucoma being the main reasons for it. Patients with unilateral PFV and type II PA could be good candidates for this combined surgical procedure., (Copyright © 2016 Sociedad Española de Oftalmología. Publicado por Elsevier España, S.L.U. All rights reserved.)
- Published
- 2017
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