1. [Moebius syndrome: therapeutic proposals from 2 cases].
- Author
-
Braye F, Souchere B, Franc C, and Freidel M
- Subjects
- Adolescent, Adult, Cranial Nerve Diseases psychology, Cranial Nerve Diseases surgery, Facial Expression, Facial Paralysis psychology, Facial Paralysis surgery, Female, Humans, Interpersonal Relations, Male, Malocclusion, Angle Class II surgery, Malocclusion, Angle Class III surgery, Ophthalmoplegia psychology, Ophthalmoplegia surgery, Osteotomy methods, Osteotomy, Le Fort, Paralysis congenital, Paralysis surgery, Poland Syndrome pathology, Strabismus congenital, Strabismus surgery, Surgical Flaps, Syndrome, Temporal Muscle transplantation, Cranial Nerve Diseases congenital, Facial Paralysis congenital, Ophthalmoplegia congenital
- Abstract
Moebius syndrome is a congenital bilateral palsy of the sixth and seventh cranial nerves. It results a total absence of facial expression and a severe strabismus. Social life is greatly disturbed. Other anomalies may be associated, especially other cranial palsies and Poland syndrome. The etiology of this syndrome isn't clearly established. Stem necrosis secondary to a vascular deficiency is often admitted. We report two observations. We emphasize the importance of a complete maxillo-facial treatment including maxillo-mandibular anomaly. Both patient underwent orthognathic surgery. The first one for class II and the second for class III anomaly. One patient underwent a facial reanimation by temporal muscle transfer. Orthognathic surgery must be realized prior to facial reanimation. A correction of the strabismus is possible. Moebius syndrome is a rare (200 observations) but very severe malformation. Maxillofacial surgery is able to improve the morphological and relational aspect of Moebius syndrome.
- Published
- 1996