1. IgG4-related sclerosing cholangitis- A great mimicker
- Author
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Hemanta Kumar, Nayak, Sunil J, Bhat, Manas Kumar, Panigrahi, Imran, Chouhan, Chandan, Kumar, and Subash Chandra, Samal
- Subjects
Diagnosis, Differential ,Male ,Autoimmune Pancreatitis ,Cholangitis, Sclerosing ,Humans ,Female ,Immunoglobulin G4-Related Disease ,Fibrosis - Abstract
IgG4-related disease (IgG4 RD) is a multisystem disorder characterized by tumefactive (mass forming) lesions, storiform fibrosis, and IgG4-positive plasma cell infiltration. IgG4 sclerosing cholangitis (IgG4 SC) is the biliary manifestation of IgG4 RD, often in association with autoimmune pancreatitis (AIP). Here, we report two patients with IgG4-related cholangitis mimicking primary sclerosing cholangitis.
- Published
- 2019