1. Disseminated lymphangiomas as a cutaneous manifestation of Noonan syndrome.
- Author
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Pérez-Feal P, Moreiras-Arias N, Buján-Bonino C, Suárez-Peñaranda JM, and Fernández-Redondo V
- Subjects
- Administration, Oral, Adolescent, Humans, Lymphangioma pathology, Male, Penis pathology, Scrotum pathology, Skin Neoplasms pathology, Treatment Outcome, Antibiotics, Antineoplastic therapeutic use, Lymphangioma complications, Lymphangioma drug therapy, Noonan Syndrome complications, Sirolimus therapeutic use, Skin Neoplasms complications, Skin Neoplasms drug therapy
- Abstract
Lymphangioma is a known, but rare manifestation of Noonan syndrome. We present the case of disseminated and circumscribed cutaneous lymphangiomas in the context of Noonan syndrome. Oral rapamycin is a promising treatment in these extensive and morbidity-causing cases., (© 2021 British Association of Dermatologists.)
- Published
- 2022
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