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Endocardial fibroelastosis is a congenital heart disease characterized by diffuse thickening of the endocardium, this conditions a dilated cardiomyopathy in most cases or less frequent restrictive cardiomyopathy. It can be a primary pathology or secondary to other cardiac malformations, especially a stenosis or atresia of the aorta. The global incidence at birth is estimated to be 1 in 5 000 and 4 in 100 congenital heart disease. The clinical case of a 37-year-old pregnant woman is presented, who was admitted at 19.1 weeks of pregnancy in Hospital Obrero N ° 2 in Cochabamba-Bolivia, due to the prenatal ultrasound diagnosis of structural fetal heart disease, endocardial fibroelastosis. [ABSTRACT FROM AUTHOR]

Description: Congenital heart diseases are most frequent fetal malformations, with a worldwide incidence of 6-8 for 1000 born alive and 27 for 1 000 stillborn. It represents one of the main causes of death in the first 30 days of postnatal life. In studies in ultrasound studies of routine in pregnant women routine ultrasound, are structural anomalies which most overlooked. Objectives: to determine the situation of prenatal diagnosis of congenital heart diseases in a sector of the population that is dependent on the Caja Nacional de Salud. Methods: Retrospective observational and descriptive study of longitudinal cut. The population studied was 9030 patients with births attended in the Hospital Obrero N°2 CNS; 1.1% of the patients were assisted in the Centro Médico Quirúrgico Boliviano Belga. The period includes the year 2009-2012. Results: it has detected, 32 fetuses with isolated cardiac pathology or as main anomaly (3.5 per 1 000 live births). Obtained the postnatal confirmation in 94%; in five (15%) patients found other additional heart defects in the neonatal exploration. Conclusions: the antenatal diagnosis of complex congenital heart diseases can modify the postnatal prognosis and it allows to schedule the birth canal adequate preparation to receive the newborn or sending to a specialized center and is fully justified all efforts that improve its detection. [ABSTRACT FROM AUTHOR]

Prune belly syndrome is a rare congenital anomaly, characterized by having: hypoplasia of abdominal wall muscles, urinary tract anomalies and bilateral cryptorchidism, clinical triggers in newborns varies, depending primarily on the degree of disturbance urinary system. Ultrasonography is the method of choice in prenatal diagnosis. The prenatal management of this picture, is aimed primarily at improving renal function and lung being the treatment of choice vesico-amniotic decompression early through the placement of a double pigtail catheter. This article presents 2 cases showing the main clinical presentations, diagnostic ultrasound and prenatal intrauterine and postnatal management of this condition. [ABSTRACT FROM AUTHOR]