1. Sudden onset of paraplegia caused by hemorrhagic spinal epidural angiolipoma. A case report.
- Author
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Akhaddar A, Albouzidi A, Elmostarchid B, Gazzaz M, and Boucetta M
- Subjects
- Angiolipoma pathology, Angiolipoma physiopathology, Back Pain etiology, Decompression, Surgical, Diagnosis, Differential, Disease Progression, Epidural Space pathology, Epidural Space physiopathology, Hematoma, Epidural, Spinal pathology, Hematoma, Epidural, Spinal physiopathology, Hemorrhage pathology, Hemorrhage physiopathology, Humans, Laminectomy, Magnetic Resonance Imaging, Male, Middle Aged, Paraplegia pathology, Paraplegia physiopathology, Spinal Cord pathology, Spinal Cord physiopathology, Spinal Cord Compression pathology, Spinal Cord Compression physiopathology, Spinal Neoplasms pathology, Spinal Neoplasms physiopathology, Spine pathology, Spine physiopathology, Thoracic Vertebrae pathology, Thoracic Vertebrae physiopathology, Treatment Outcome, Angiolipoma complications, Hematoma, Epidural, Spinal etiology, Hemorrhage complications, Paraplegia etiology, Spinal Cord Compression etiology, Spinal Neoplasms complications
- Abstract
Spinal epidural angiolipoma is a rare benign tumor containing vascular and mature adipose elements. A slow progressive clinical course was mostly presented and rarely a fluctuating course during pregnancy. The authors report the original case of spontaneous spinal epidural bleeding resulting from thoracic epidural angiolipoma who presented with hyperacute onset of paraplegia, simulating an extradural hematoma. The patient was admitted with sudden non-traumatic hyperacute paraplegia during a prolonged walk. Neurologic examination showed sensory loss below T6 and bladder disturbances. Spinal MRI revealed a non-enhanced heterogeneous thoracic epidural lesion, extending from T2 to T3. A bilateral T2-T4 laminectomy was performed to achieve resection of a lipomatous tumor containing area of spontaneous hemorrhage. The postoperative course was uneventful with complete neurologic recovery. Histologic examination revealed the tumor as an angiolipoma. Because the prognosis after rapid surgical management of this lesion is favorable, the diagnosis of spinal angiolipoma with bleeding should be considered in the differential diagnosis of hyperacute spinal cord compression.
- Published
- 2008
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