246 results on '"Amthor, Helge"'
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2. Safety and efficacy of tamoxifen in boys with Duchenne muscular dystrophy (TAMDMD): a multicentre, randomised, double-blind, placebo-controlled, phase 3 trial
3. Diagnostic interest of whole-body MRI in early- and late-onset LAMA2 muscular dystrophies: a large international cohort
4. Severe ACTA1-related nemaline myopathy: intranuclear rods, cytoplasmic bodies, and enlarged perinuclear space as characteristic pathological features on muscle biopsies
5. Distinct whole-body muscle MRI imaging patterns in PAX7-congenital myopathy: A case report.
6. Treadmill running and mechanical overloading improved the strength of the plantaris muscle in the dystrophin‐desmin double knockout (DKO) mouse.
7. The role of myostatin during avian muscle development
8. Safety and efficacy of tamoxifen in boys with Duchenne muscular dystrophy (TAMDMD): a multicentre, randomised, double-blind, placebo-controlled, phase 3 trial
9. Asymmetric muscle weakness due to ACTA1 mosaic mutations
10. Prognosis of Right Ventricular Systolic Dysfunction in Patients With Duchenne Muscular Dystrophy
11. Human muscle-derived CLEC14A-positive cells regenerate muscle independent of PAX7
12. Inhibitory SMAD6 interferes with BMP dependent generation of muscle progenitor cells and perturbs proximodistal pattern of murine limb muscles
13. Quels critères d’évaluation sensibles au changement pour le suivi de la motricité de patients atteints de la maladie de Pompe. Un projet soutenu par la SFP 2023
14. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle
15. Blockade of ActRIIB Signaling Triggers Muscle Fatigability and Metabolic Myopathy
16. Mutations in KLHL40 Are a Frequent Cause of Severe Autosomal-Recessive Nemaline Myopathy
17. Muscle Hypertrophy Driven by Myostatin Blockade Does Not Require Stem/Precursor-Cell Activity
18. Diagnostic interest of whole-body MRI in early- and late-onset LAMA2 muscular dystrophies:a large international cohort
19. Phenotypic spectrum and genomics of undiagnosed arthrogryposis multiplex congenita
20. Lack of Myostatin Results in Excessive Muscle Growth but Impaired Force Generation
21. Functional correction in mouse models of muscular dystrophy using exon-skipping tricyclo-DNA oligomers
22. Effect of constitutive inactivation of the myostatin gene on the gain in muscle strength during postnatal growth in two murine models
23. Current advances in the development of therapies for neuromuscular disorders based on myostatin signalling, 3rd International Institute of Myology Workshop, Paris, September 12th, 2008
24. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle.
25. Determinants of diaphragm inspiratory motion, diaphragm thickening and its performance for predicting respiratory restrictive pattern in Duchenne muscular dystrophy
26. Loss of a single allele for Ku80 leads to progenitor dysfunction and accelerated aging in skeletal muscle
27. Myostatin knockout mice increase oxidative muscle phenotype as an adaptive response to exercise
28. A muscle growth promoting treatment based on the attenuation of activin/myostatin signalling in young mice results in long-term testicular abnormalities
29. Very Low Residual Dystrophin Quantity Is Associated with Milder Dystrophinopathy
30. Diagnostic interest of whole-body MRI in early- and late-onset LAMA2 muscular dystrophies: a large international cohort
31. Association between prophylactic angiotensin-converting enzyme inhibitors and overall survival in Duchenne muscular dystrophy-analysis of registry data
32. Diminution in sperm quantity and quality in mouse models of Duchenne Muscular Dystrophy induced by a myostatin-based muscle growth-promoting intervention
33. Activin A inhibits formation of skeletal muscle during chick development
34. Phenotypic spectrum and genomics of undiagnosed arthrogryposis multiplex congenita
35. Follistatin complexes Myostatin and antagonises Myostatin-mediated inhibition of myogenesis
36. The regulation and action of Myostatin as a negative regulator of muscle development during avian embryogenesis
37. Follistatin regulates bone morphogenetic protein-7 (BMP-7) activity to stimulate embryonic muscle growth
38. Exercise training attenuates the hypermuscular phenotype and restores skeletal muscle function in the myostatin null mouse
39. A muscle growth-promoting treatment based on the attenuation of activin/myostatin signalling results in long-term testicular abnormalities
40. BMP Signaling Determines the Proximodistal Pattern of Limb Muscles by Spatiotemporal Control of Myogenic Progenitor Cells
41. Inhibition of Activin/Myostatin signalling induces skeletal muscle hypertrophy but impairs mouse testicular development
42. The function of Myostatin and strategies of Myostatin blockade—new hope for therapies aimed at promoting growth of skeletal muscle
43. Referee report. For: Single-transcript multiplex in situ hybridisation reveals unique patterns of dystrophin isoform expression in the developing mammalian embryo [version 1; peer review: 1 approved, 1 approved with reservations]
44. Mouse model carrying H222P-Lmna mutation develops muscular dystrophy and dilated cardiomyopathy similar to human striated muscle laminopathies
45. The expression and regulation of Follistatin and a Follistatin-like gene during avian somite compartmentalization and myogenesis
46. Albumin targeting of damaged muscle fibres in the mdx mouse can be monitored by MRI
47. Determinants of diaphragm inspiratory motion, diaphragm thickening, and its performance for predicting respiratory restrictive pattern in Duchenne muscular dystrophy.
48. Airway nitric oxide in Duchenne muscular dystrophy
49. SIX1 and SIX4 homeoproteins regulate PAX7+ progenitor cell properties during fetal epaxial myogenesis
50. 240th ENMC workshop: The involvement of skeletal muscle stem cells in the pathology of muscular dystrophies 25–27 January 2019, Hoofddorp, The Netherlands
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