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1. Microglia-Impaired Phagocytosis Contributes to the Epileptogenesis in a Mouse Model of Dravet Syndrome.

2. SCN1A intronic variants impact on Nav1.1 protein expression and sodium channel function, and associated with epilepsy phenotypic severity.

3. Abnormal increased mTOR signaling regulates seizure threshold in Dravet syndrome.

4. Epigenetic insights into GABAergic development in Dravet Syndrome iPSC and therapeutic implications.

5. Opposing effects of the purinergic P2X7 receptor on seizures in neurons and microglia in male mice.

6. A high seizure burden increases several prostaglandin species in the hippocampus of a Scn1a +/- mouse model of Dravet syndrome.

7. Ndnf Interneuron Excitability Is Spared in a Mouse Model of Dravet Syndrome.

8. Modulating Endoplasmic Reticulum Chaperones and Mutant Protein Degradation in GABRG2(Q390X) Associated with Genetic Epilepsy with Febrile Seizures Plus and Dravet Syndrome.

9. Integrating Proteomics and Transcriptomics Reveals the Potential Pathways of Hippocampal Neuron Apoptosis in Dravet Syndrome Model Mice.

10. Microglia Mitigate Neuronal Activation in a Zebrafish Model of Dravet Syndrome.

11. Anticonvulsant effect of equilibrative nucleoside transporters 1 inhibitor in a mouse model of Dravet syndrome.

12. Biophysical characterization and modelling of SCN1A gain-of-function predicts interneuron hyperexcitability and a predisposition to network instability through homeostatic plasticity.

13. Heterozygous deletion of Gpr55 does not affect a hyperthermia-induced seizure, spontaneous seizures or survival in the Scn1a+/- mouse model of Dravet syndrome.

14. Experimental and Bioinformatic Insights into the Effects of Epileptogenic Variants on the Function and Trafficking of the GABA Transporter GAT-1.

15. The endocannabinoid system impacts seizures in a mouse model of Dravet syndrome.

16. Chronic partial TrkB activation reduces seizures and mortality in a mouse model of Dravet syndrome.

17. Ameliorating Effect of Umbilical Cord Mesenchymal Stem Cells in a Human Induced Pluripotent Stem Cell Model of Dravet Syndrome.

18. Scn1a gene reactivation after symptom onset rescues pathological phenotypes in a mouse model of Dravet syndrome.

19. MRS-measured glutamate versus GABA reflects excitatory versus inhibitory neural activities in awake mice.

20. Neuroserpin: structure, function, physiology and pathology.

21. Proteomic signature of the Dravet syndrome in the genetic Scn1a-A1783V mouse model.

22. Efficacy of Fenfluramine and Norfenfluramine Enantiomers and Various Antiepileptic Drugs in a Zebrafish Model of Dravet Syndrome.

23. Two-photon calcium imaging of seizures in awake, head-fixed mice.

24. Somatostatin-expressing parafacial neurons are CO 2 /H + sensitive and regulate baseline breathing.

25. The ALOXE3 gene variants from patients with Dravet syndrome decrease gene expression and enzyme activity.

26. Atypical myelinogenesis and reduced axon caliber in the Scn1a variant model of Dravet syndrome: An electron microscopy pilot study of the developing and mature mouse corpus callosum.

27. Developmental alterations in firing properties of hippocampal CA1 inhibitory and excitatory neurons in a mouse model of Dravet syndrome.

28. The E3 ubiquitin ligase MARCHF6 as a metabolic integrator in cholesterol synthesis and beyond.

29. A selective Na V 1.1 activator with potential for treatment of Dravet syndrome epilepsy.

30. Electrophysiological Alterations of Pyramidal Cells and Interneurons of the CA1 Region of the Hippocampus in a Novel Mouse Model of Dravet Syndrome.

31. Familial cortical myoclonic tremor with epilepsy: TTTCA/TTTTA repeat expansions and expanding phenotype in two Chinese families.

32. NaV1.1 and NaV1.6 selective compounds reduce the behavior phenotype and epileptiform activity in a novel zebrafish model for Dravet Syndrome.

33. New insights into the early mechanisms of epileptogenesis in a zebrafish model of Dravet syndrome.

34. GluN2A NMDA Receptor Enhancement Improves Brain Oscillations, Synchrony, and Cognitive Functions in Dravet Syndrome and Alzheimer's Disease Models.

35. Transcriptomes of Dravet syndrome iPSC derived GABAergic cells reveal dysregulated pathways for chromatin remodeling and neurodevelopment.

36. Coadministered cannabidiol and clobazam: Preclinical evidence for both pharmacodynamic and pharmacokinetic interactions.

37. Potentiating α 2 subunit containing perisomatic GABA A receptors protects against seizures in a mouse model of Dravet syndrome.

38. Vasoactive intestinal peptide-expressing interneurons are impaired in a mouse model of Dravet syndrome.

39. Mitochondrial Regulation of the Hippocampal Firing Rate Set Point and Seizure Susceptibility.

40. Delayed maturation of GABAergic signaling in the Scn1a and Scn1b mouse models of Dravet Syndrome.

41. Stiripentol protects against calcium oxalate nephrolithiasis and ethylene glycol poisoning.

42. In vivo, in vitro and in silico correlations of four de novo SCN1A missense mutations.

43. RNA-seq Analysis of the SCN1A-KO Model based on CRISPR/Cas9 Genome Editing Technology.

44. Gene expression profiling in a mouse model of Dravet syndrome.

45. Elimination of amyloid precursor protein in senile plaques in the brain of a patient with Alzheimer-type dementia and Down syndrome.

46. A novel GABAergic dysfunction in human Dravet syndrome.

47. Cannabis for the Treatment of Epilepsy: an Update.

48. Selective Na V 1.1 activation rescues Dravet syndrome mice from seizures and premature death.

49. Population Pharmacokinetics of Stiripentol in Paediatric Patients with Dravet Syndrome Treated with Stiripentol, Valproate and Clobazam Combination Therapy.

50. Differential effects on sodium current impairments by distinct SCN1A mutations in GABAergic neurons derived from Dravet syndrome patients.

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