1. Natural history of a systemic right ventricle
- Author
-
A. Kirsten Finucane, Peter Ruygrok, Jean Lee, and Ivor L. Gerber
- Subjects
Male ,medicine.medical_specialty ,Heart Ventricles ,Transposition of Great Vessels ,Ventricular Dysfunction, Right ,030204 cardiovascular system & hematology ,03 medical and health sciences ,0302 clinical medicine ,Internal medicine ,Internal Medicine ,medicine ,Humans ,030212 general & internal medicine ,Heart Failure ,business.industry ,Middle Aged ,medicine.disease ,Atrial switch ,Natural history ,Transplantation ,Treatment Outcome ,medicine.anatomical_structure ,Ventricle ,Great arteries ,Heart failure ,Cardiology ,Heart Transplantation ,Right atrium ,business ,Medical therapy - Abstract
The natural history of a systemic right ventricle after an atrial switch procedure has yet to be fully characterised. We describe the case of the longest surviving patient at our institution who underwent a Mustard Baffle correction for dextro-transposition of great arteries in childhood. Over following decades he was reviewed regularly with deteriorating systemic right ventricle function. At around 50 years of age he developed worsening heart failure on maximal medical therapy. He was subsequently assessed for cardiac transplantation which he underwent successfully at the age of 55 years.
- Published
- 2019