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Hemitruncus arteriosus is a rare cardiovascular malformation in which one of the pulmonary arteries anomalously originates from the aorta. Left hemitruncus arteriosus, defined as the origination of the left pulmonary artery from the aorta, is less common than right hemitruncus arteriosus. In this study, we report the case of a neonate diagnosed with left hemitruncus arteriosus, ventricular septal defect, and atrial septal defect who underwent successful surgical treatment.

Sol hemitrunkus (sol pulmoner arterin aort kokeninden ayrilma anomalisi) sag hemitrunkusa gore daha nadir gorulur. Fallot tetralojisi ile sol hemitrunkus birlikteliginde sol pulmoner yatakta erken gelisebilecek pulmoner vaskuler obstruktif hastaligi onlemek icin erken tani cok onemlidir. Bildigimiz kadariyla, literaturde, Fallot tetralojisi ve sol hemitrunkus birlikteliginde ilk dekatta yapilan ve yasayan bes sol hemitrunkuslu olgu mevcuttur. Asamali cerrahi yapilarak tam duzeltme saglanan herhangi bir pediatrik olgu literaturde henuz bildirilmemistir. Bu yazida, palyatif sol pulmoner band ameliyatinin ardindan total tamir ile asamali duzeltme cerrahisi yapilan gec tani konulmus Fallot tetralojili ve sol hemitrunkuslu bir yasinda kiz cocugu sunuldu. Anah tar soz cuk ler: Cocuk; dogustan kalp hastaligi; hemitrunkus; pulmoner hipertansiyon; sag arkus aort; selektif pulmoner banding; Fallot tetralojisi. Left hemitruncus (aortic anomalous origin of the left pulmonary artery) is relatively rare than the right hemitruncus. Early diagnosis is critical to prevent early occurrence of pulmonary vascular obstructive disease in the left pulmonary bed in patients with tetralogy of Fallot presenting with left hemitruncus arteriosus. To the best of our knowledge, there are only five surviving cases with left hemitruncus and tetralogy of Fallot who were operated in the first decade of life in the literature. Any pediatric case undergoing staged surgery with full recovery has not been reported yet in the literature. In this article, we report a one-year-old girl with tetralogy of Fallot and left hemitruncus with a late diagnosis who underwent staged correction surgery with palliative left pulmonary artery banding followed by total repair.

WOS: 000219058200014, Hemitruncus is an uncommon congenital defect in which a pulmonary artery (PA) branch originates abnormally from the ascending aorta. Left hemitruncus is less common than a right hemitruncus. In this report, we present an isolated left hemitruncus in a neonate who showed progressive respiratory distress in the second week following delivery. At 21 days of age, the patient underwent total surgical correction of the defect, during which a direct end-to-side anastomosis to main PA without conduit interposition was employed. After a prolonged intubation period with pneumonia, the patient was discharged from hospital on the 17th postoperative day.

Hemitruncus is an uncommon congenital anomaly that has been described in isolation or in association with other congenital cardiac malformations. This report describes a rare case of left hemitruncus with tetralogy of Fallot and a right-sided aortic arch. The patient presented to us in the early second decade. The diagnosis was suspected with echocardiography and confirmed with cardiac catheterization. The patient underwent successful surgical correction of the anomaly.

This report presents a case of a left hemitruncus and tetralogy of Fallot. The diagnosis was first made by means of echocardiography and confirmed with cardiac catheterization thereafter. To the authors' knowledge, this patient is the fourth-longest-term survivor so far reported in the medical literature. A significant improvement has been observed after surgical correction of the anomaly, and the patient was free of symptoms at the 6-mo follow-up examination.

The diagnosis of left hemitruncus and large patent ductus arteriosus was made by magnetic resonance imaging in an adult patient with recurrent haemoptysis and dyspnoea on exertion. Previous cardiac catheterization and echocardiography failed to establish the complete diagnosis. Magnetic resonance imaging using spin-echo and gradient-echo pulse sequences is a useful imaging modality to evaluate anatomical and functional abnormalities in patients with complex congenital heart disease.