7 results on '"Rautenberg G"'
Search Results
2. The Fluorescence Detector of the Pierre Auger Observatory
- Author
-
The Pierre Auger Collaboration, Abraham, J., Abreu, P., Aglietta, M., Aguirre, C., Ahn, E. J., Allard, D., Allekotte, I., Allen, J., Allison, P., Alvarez-Muñiz, J., Ambrosio, M., Anchordoqui, L., Andringa, S., Anzalone, A., Aramo, C., Arganda, E., Argirò, S., Arisaka, K., Arneodo, F., Arqueros, F., Asch, T., Asorey, H., Assis, P., Aublin, J., Ave, M., Avila, G., Bacher, A., Bäcker, T., Badagnani, D., Barber, K. B., Barbosa, A. F., Barbosa, H. J. M., Barenthien, N., Barroso, S. L. C., Baughman, B., Bauleo, P., Beatty, J. J., Beau, T., Becker, B. R., Becker, K. H., Bellétoile, A., Bellido, J. A., BenZvi, S., Berat, C., Bernardini, P., Bertou, X., Biermann, P. L., Billoir, P., Blanch-Bigas, O., Blanco, F., Bleve, C., Blümer, H., Boháčová, M., Bollmann, E., Bolz, H., Bonifazi, C., Bonino, R., Borodai, N., Bracci, F., Brack, J., Brogueira, P., Brown, W. C., Bruijn, R., Buchholz, P., Bueno, A., Burton, R. E., Busca, N. G., Caballero-Mora, K. S., Caramete, D. CaminL., Caruso, R., Carvalho, W., Castellina, A., Castro, J., Catalano, O., Cazon, L., Cester, R., Chauvin, J., Chiavassa, A., Chinellato, J. A., Chou, A., Chudoba, J., Chye, J., Clark, P. D. J., Clay, R. W., Colombo, E., Conceição, R., Connolly, B., Contreras, F., Coppens, J., Cordero, A., Cordier, A., Cotti, U., Coutu, S., Covault, C. E., Creusot, A., Criss, A., Cronin, J. W., Cuautle, J., Curutiu, A., Dagoret-Campagne, S., Dallier, R., Daudo, F., Daumiller, K., Dawson, B. R., de Almeida, R. M., De Domenico, M., De Donato, C., de Jong, S. J., De La Vega, G., Junior, W. J. M. de Mello, Neto, J. R. T. de Mello, De Mitri, I., de Souza, V., de Vries, K. D., Decerprit, G., del Peral, L., Deligny, O., Della Selva, A., Fratte, C. Delle, Dembinski, H., Di Giulio, C., Diaz, J. C., Diep, P. N., Dobrigkeit, C., D'Olivo, J. C., Dong, P. N., Dornic, D., Dorofeev, A., Anjos, J. C. dos, Dova, M. T., D'Urso, D., Dutan, I., DuVernois, M. A., Engel, R., Erdmann, M., Escobar, C. O., Etchegoyen, A., Luis, P. Facal San, Falcke, H., Farrar, G., Fauth, A. C., Fazzini, N., Ferrer, F., Ferrero, A., Fick, B., Filevich, A., Filipčič, A., Fleck, I., Fliescher, S., Fonte, R., Fracchiolla, C. E., Fraenkel, E. D., Fulgione, W., Gamarra, R. F., Gambetta, S., García, B., Gámez, D. García, Garcia-Pinto, D., Garrido, X., Geenen, H., Gelmini, G., Gemmeke, H., Ghia, P. L., Giaccari, U., Gibbs, K., Giller, M., Gitto, J., Glass, H., Goggin, L. M., Gold, M. S., Golup, G., Albarracin, F. Gomez, Berisso, M. Gómez, Vitale, P. F. Gomez, Gonçalves, P., Amaral, M. Gonçalves do, Gonzalez, D., Gonzalez, J. G., Góra, D., Gorgi, A., Gouffon, P., Grashorn, E., Grassi, V., Grebe, S., Grigat, M., Grillo, A. F., Grygar, J., Guardincerri, Y., Guardone, N., Guerard, C., Guarino, F., Gumbsheimer, R., Guedes, G. P., Gutiérrez, J., Hague, J. D., Halenka, V., Hansen, P., Harari, D., Harmsma, S., Hartmann, S., Harton, J. L., Haungs, A., Healy, M. D., Hebbeker, T., Hebrero, G., Heck, D., Hojvat, C., Holmes, V. C., Homola, P., Hofman, G., Hörandel, J. R., Horneffer, A., Horvat, M., Hrabovský, M., Hucker, H., Huege, T., Hussain, M., Iarlori, M., Insolia, A., Ionita, F., Italiano, A., Jiraskova, S., Kaducak, M., Kampert, K. H., Karova, T., Kasper, P., Kégl, B., Keilhauer, B., Kemp, E., Kern, H., Kieckhafer, R. M., Klages, H. O., Kleifges, M., Kleinfeller, J., Knapik, R., Knapp, J., Koang, D. -H., Kopmann, A., Krieger, A., Krömer, O., Kruppke-Hansen, D., Kuempel, D., Kunka, N., Kusenko, A., La Rosa, G., Lachaud, C., Lago, B. L., Lautridou, P., Leão, M. S. A. B., Lebrun, D., Lebrun, P., Lee, J., de Oliveira, M. A. Leigui, Lemiere, A., Letessier-Selvon, A., Leuthold, M., Lhenry-Yvon, I., López, R., Agüera, A. Lopez, Louedec, K., Bahilo, J. Lozano, Lucero, A., Lyberis, H., Maccarone, M. C., Macolino, C., Maldera, S., Malek, M., Mandat, D., Mantsch, P., Marchetto, F., Mariazzi, A. G., Maris, I. C., Falcon, H. R. Marquez, Martello, D., Martineau, O., Bravo, O. Martínez, Mathes, H. J., Matthews, J., Matthews, J. A. J., Matthiae, G., Maurizio, D., Mazur, P. O., McEwen, M., McNeil, R. R., Medina-Tanco, G., Melissas, M., Melo, D., Menichetti, E., Menshikov, A., Meyhandan, R., Micheletti, M. I., Miele, G., Miller, W., Miramonti, L., Mollerach, S., Monasor, M., Ragaigne, D. Monnier, Montanet, F., Morales, B., Morello, C., Moreno, J. C., Morris, C., Mostafá, M., Moura, C. A., Mucchi, M., Mueller, S., Muller, M. A., Mussa, R., Navarra, G., Navarro, J. L., Navas, S., Necesal, P., Nellen, L., Nerling, F., Newman-Holmes, C., Newton, D., Nhung, P. T., Nicotra, D., Nierstenhoefer, N., Nitz, D., Nosek, D., Nožka, L., Nyklicek, M., Oehlschläger, J., Olinto, A., Oliva, P., Olmos-Gilbaja, V. M., Ortiz, M., Ortolani, F., Oßwald, B., Pacheco, N., Selmi-Dei, D. Pakk, Palatka, M., Pallotta, J., Parente, G., Parizot, E., Parlati, S., Pastor, S., Patel, M., Paul, T., Pavlidou, V., Payet, K., Pech, M., Pȩkala, J., Pepe, I. M., Perrone, L., Pesce, R., Petermann, E., Petrera, S., Petrinca, P., Petrolini, A., Petrov, Y., Petrovic, J., Pfendner, C., Pichel, A., Piegaia, R., Pierog, T., Pimenta, M., Pinto, T., Pirronello, V., Pisanti, O., Platino, M., Pochon, J., Ponce, V. H., Pontz, M., Pouryamout, J., Prado Jr., L., Privitera, P., Prouza, M., Quel, E. J., Rautenberg, G. Raia J., Ravel, O., Ravignani, D., Redondo, A., Reis, H. C., Reucroft, S., Revenu, B., Rezende, F. A. S., Ridky, J., Riggi, S., Risse, M., Rivière, C., Rizi, V., Robledo, C., Roberts, M. D., Rodriguez, G., Martino, J. Rodriguez, Rojo, J. Rodriguez, Rodriguez-Cabo, I., Rodríguez-Frías, M. D., Ros, G., Rosado, J., Rossler, T., Roth, M., Rouillé-d'Orfeuil, B., Roulet, E., Rovero, A. C., Salamida, F., b, H. Salazar, Salina, G., Sánchez, F., Santander, M., Santo, C. E., Santos, E. M., Sarazin, F., Sarkar, S., Sato, R., Scharf, N., Scherini, V., Schieler, H., Schiffer, P., Schmidt, G. Schleif A., Schmidt, F., Schmidt, T., Scholten, O., Schoorlemmer, H., Schovancova, J., Schovánek, P., Schroeder, F., Schulte, S., Schüssler, F., Schuster, D., Sciutto, S. J., Scuderi, M., Segreto, A., Semikoz, D., Sequieros, G., Settimo, M., Shellard, R. C., Sidelnik, I., Siffert, B. B., Smiałkowski, A., Šmída, R., Smith, A. G. K., Smith, B. E., Snow, G. R., Sommers, P., Sorokin, J., Spinka, H., Squartini, R., Strazzeri, E., Stutz, A., Suarez, F., Suomijärvi, T., Supanitsky, A. D., Sutherland, M. S., Swain, J., Szadkowski, Z., Tamashiro, A., Tamburro, A., Tarutina, T., Taşcău, O., Tcaciuc, R., Tcherniakhovski, D., Thao, N. T., Thomas, D., Ticona, R., Tiffenberg, J., Timmermans, C., Tkaczyk, W., Peixoto, C. J. Todero, Tomé, B., Tonachini, A., Torres, I., Trapani, P., Travnicek, P., Tridapalli, D. B., Tristram, G., Trovato, E., Tuci, V., Tueros, M., Tusi, E., Ulrich, R., Unger, M., Urban, M., Galicia, J. F. Valdés, Valiño, I., Valore, L., Berg, A. M. van den, Vázquez, J. R., Vázquez, R. A., Veberič, D., Velarde, A., Venters, T., Verzi, V., Videla, M., Villaseñor, L., Vitali, G., Vorobiov, S., Voyvodic, L., Wahlberg, H., Wahrlich, P., Wainberg, O., Warner, D., Westerhoff, S., Whelan, B. J., Wild, N., Wiebusch, C., Wieczorek, G., Wiencke, L., Wilczyńska, B., Wilczyński, H., Wileman, C., Winnick, M. G., Wörner, G., Wu, H., Wundheiler, B., Yamamoto, T., Younk, P., Yuan, G., Yushkov, A., Zas, E., Zavrtanik, D., Zavrtanik, M., Zaw, I., b, A. Zepeda, and Ziolkowski, M.
- Subjects
Astrophysics - Instrumentation and Methods for Astrophysics - Abstract
The Pierre Auger Observatory is a hybrid detector for ultra-high energy cosmic rays. It combines a surface array to measure secondary particles at ground level together with a fluorescence detector to measure the development of air showers in the atmosphere above the array. The fluorescence detector comprises 24 large telescopes specialized for measuring the nitrogen fluorescence caused by charged particles of cosmic ray air showers. In this paper we describe the components of the fluorescence detector including its optical system, the design of the camera, the electronics, and the systems for relative and absolute calibration. We also discuss the operation and the monitoring of the detector. Finally, we evaluate the detector performance and precision of shower reconstructions., Comment: 53 pages. Submitted to Nuclear Instruments and Methods in Physics Research Section A
- Published
- 2009
- Full Text
- View/download PDF
3. Length–Weight Relationships and Body Condition Indices of a South American Bioindicator, the Native Neotropical Fish Species, Cnesterodon decemmaculatus (Poeciliidae)
- Author
-
Zambrano, M. J., primary, Bonifacio, A. F., additional, Brito, J. M., additional, Rautenberg, G. E., additional, and Hued, A. C., additional
- Published
- 2023
- Full Text
- View/download PDF
4. Guidelines for incorporating scientific knowledge and practice on rare diseases into higher education: neuronal ceroid lipofuscinoses as a model disorder model disorder
- Author
-
Kohan, R., Cismondi, I.A., Adams, H., Bond, M., Brown, R., Cooper, J.D., Krupnik de Hidalgo, P., Kleine Holthaus, S.M., Mole, S.E., Mugnaini, J., Oller de Ramirez, A.M., Pesaola, F., Platt, F.M., Noher de Halac, I., and Rautenberg, G.
- Subjects
Research ,education ,Patient advocacy ,Neuronal ceroid-lipofuscinoses ,Rare diseases ,Education - Abstract
This article addresses the educational issues associated with rare diseases (RD) and in particular the Neuronal Ceroid Lipofuscinoses (NCLs, or CLN diseases) in the curricula of Health Sciences and Professional's Training Programs. Our aim is to develop guidelines for improving scientific knowledge and practice in higher education and continuous learning programs. Rare diseases (RD) are collectively common in the general populationwith 1 in 17 people affected by a RDin their lifetime. Inherited defects in genes involved in metabolism are the commonest group of RD with over 8000 known inborn errors of metabolism. The majority of these diseases are neurodegenerative including the NCLs. Any professional training program on NCL must take into account the medical, social and economic burdens related to RDs. To address these challenges and find solutions to themit is necessary that individuals in the government and administrative authorities, academia, teaching hospitals and medical schools, the pharmaceutical industry, investment community and patient advocacy groups all work together to achieve these goals. The logistical issues of including RD lectures in university curricula and in continuing medical education should reflect its complex nature. To evaluate the state of education in the RD field, a summary should be periodically up dated in order to assess the progress achieved in each country that signed up to the international conventions addressing RD issues in society. It is anticipated that auditing current practice will lead to higher standards and provide a framework for those educators involved in establishing RD teaching programs world-wide. publishedVersion
- Published
- 2015
5. A translational research experience in Argentina
- Author
-
Kohan, R., Pesaola, F., Guelbert, N., Pons, P., Oller de Ramirez, A.M., Rautenberg, G., Becerra, A., Sims, K., Xin, W., and Cismondi, I.A.
- Subjects
Neuronal ceroid-lipofuscinoses ,Algorithms ,Anatomy and histology ,Enzymes - Abstract
Background: The Argentinean programwas initiatedmore than a decade ago as the first experience of systematic translational research focused on NCL in Latin America. The aim was to overcome misdiagnoses and underdiagnoses in the region. Subjects: 216 NCL suspected individuals from 8 different countries and their direct family members. Methods: Clinical assessment, enzyme testing, electron microscopy, and DNA screening. Results and discussion: 1) The study confirmed NCL disease in 122 subjects. Phenotypic studies comprised epileptic seizures and movement disorders, ophthalmology, neurophysiology, image analysis, rating scales, enzyme testing, and electron microscopy, carried out under a consensus algorithm; 2) DNA screening and validation of mutations in genes PPT1 (CLN1), TPP1 (CLN2), CLN3, CLN5, CLN6, MFSD8 (CLN7), and CLN8: characterization of variant types, novel/knownmutations and polymorphisms; 3) Progress of the epidemiological picture in Latin America; and 4) NCL-like pathology studies in progress. The Translational Research Program was highly efficient in addressing the misdiagnosis/underdiagnosis in the NCL disorders. The study of “orphan diseases” in a public administrated hospital should be adopted by the health systems, as it positively impacts upon the family's quality of life, the collection of epidemiological data, and triggers research advances. This article is part of a Special Issue entitled: “Current Research on the Neuronal Ceroid Lipofuscinoses (Batten Disease)” publishedVersion
- Published
- 2015
6. Guidelines for incorporating scientific knowledge and practice on rare diseases into higher education: neuronal ceroid lipofuscinoses as a model disorder.
- Author
-
Cismondi IA, Kohan R, Adams H, Bond M, Brown R, Cooper JD, de Hidalgo PK, Holthaus SM, Mole SE, Mugnaini J, de Ramirez AM, Pesaola F, Rautenberg G, Platt FM, and Noher de Halac I
- Abstract
This article addresses the educational issues associated with rare diseases (RD) and in particular the Neuronal Ceroid Lipofuscinoses (NCLs, or CLN diseases) in the curricula of Health Sciences and Professional's Training Programs. Our aim is to develop guidelines for improving scientific knowledge and practice in higher education and continuous learning programs. Rare diseases (RD) are collectively common in the general population with 1 in 17 people affected by a RD in their lifetime. Inherited defects in genes involved in metabolism are the commonest group of RD with over 8000 known inborn errors of metabolism. The majority of these diseases are neurodegenerative including the NCLs. Any professional training program on NCL must take into account the medical, social and economic burdens related to RDs. To address these challenges and find solutions to them it is necessary that individuals in the government and administrative authorities, academia, teaching hospitals and medical schools, the pharmaceutical industry, investment community and patient advocacy groups all work together to achieve these goals. The logistical issues of including RD lectures in university curricula and in continuing medical education should reflect its complex nature. To evaluate the state of education in the RD field, a summary should be periodically up dated in order to assess the progress achieved in each country that signed up to the international conventions addressing RD issues in society. It is anticipated that auditing current practice will lead to higher standards and provide a framework for those educators involved in establishing RD teaching programs world-wide., (Copyright © 2015 Elsevier B.V. All rights reserved.)
- Published
- 2015
- Full Text
- View/download PDF
7. The neuronal ceroid lipofuscinoses program: A translational research experience in Argentina.
- Author
-
Kohan R, Pesaola F, Guelbert N, Pons P, Oller-Ramírez AM, Rautenberg G, Becerra A, Sims K, Xin W, Cismondi IA, and Noher de Halac I
- Abstract
Background: The Argentinean program was initiated more than a decade ago as the first experience of systematic translational research focused on NCL in Latin America. The aim was to overcome misdiagnoses and underdiagnoses in the region., Subjects: 216 NCL suspected individuals from 8 different countries and their direct family members., Methods: Clinical assessment, enzyme testing, electron microscopy, and DNA screening., Results and Discussion: 1) The study confirmed NCL disease in 122 subjects. Phenotypic studies comprised epileptic seizures and movement disorders, ophthalmology, neurophysiology, image analysis, rating scales, enzyme testing, and electron microscopy, carried out under a consensus algorithm; 2) DNA screening and validation of mutations in genes PPT1 (CLN1), TPP1 (CLN2), CLN3, CLN5, CLN6, MFSD8 (CLN7), and CLN8: characterization of variant types, novel/known mutations and polymorphisms; 3) Progress of the epidemiological picture in Latin America; and 4) NCL-like pathology studies in progress. The Translational Research Program was highly efficient in addressing the misdiagnosis/underdiagnosis in the NCL disorders. The study of "orphan diseases" in a public administrated hospital should be adopted by the health systems, as it positively impacts upon the family's quality of life, the collection of epidemiological data, and triggers research advances. This article is part of a Special Issue entitled: "Current Research on the Neuronal Ceroid Lipofuscinoses (Batten Disease)"., (Copyright © 2015 Elsevier B.V. All rights reserved.)
- Published
- 2015
- Full Text
- View/download PDF
Catalog
Discovery Service for Jio Institute Digital Library
For full access to our library's resources, please sign in.