490 results on '"Stoltz, David A."'
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2. Development and Initial Characterization of Pigs with DNAI1 Mutations and Primary Ciliary Dyskinesia
3. Mucociliary Clearance is Impaired in Small Airways of Cystic Fibrosis Pigs
4. CFTR-rich ionocytes mediate chloride absorption across airway epithelia
5. Pancreatic enzymes digest obstructive meconium from cystic fibrosis pig intestines
6. Cystic Fibrosis Carrier States Are Associated With More Severe Cases of Bronchiectasis
7. INJECTABLE LONG-ACTING IVACAFTOR-LOADED POLY (LACTIDE-CO-GLYCOLIDE) MICROPARTICLE FORMULATIONS FOR THE TREATMENT OF CYSTIC FIBROSIS: IN VITRO CHARACTERIZATION AND IN VIVO PHARMACOKINETICS IN MICE
8. Cystic fibrosis carriers are at increased risk for a wide range of cystic fibrosis-related conditions
9. Early pathogenesis of cystic fibrosis gallbladder disease in a porcine model
10. Pancreatic enzymes digest obstructive meconium from cystic fibrosis pig intestines.
11. FATAL LUNG INJURY SECONDARY TO TRIMETHOPRIM-SULFAMETHOXAZOLE
12. Inflammatory cytokines TNF-[alpha] and IL-17 enhance the efficacy of cystic fibrosis transmembrane conductance regulator modulators
13. Gel-forming mucins form distinct morphologic structures in airways
14. Cystic Fibrosis Reprograms Airway Epithelial IL-33 Release and Licenses IL-33 Dependent Inflammation
15. CFTR deficiency increases Th2 cytokine production and allergic airway inflammation in mice
16. Lack of cystic fibrosis transmembrane conductance regulator disrupts fetal airway development in pigs
17. Airway acidification initiates host defense abnormalities in cystic fibrosis mice
18. Categorization Framework for Systems Innovation in Eco Cities
19. Glycogen depletion can increase the specificity of mucin detection in airway tissues
20. Tromethamine improves mucociliary clearance in cystic fibrosis pigs
21. Pulmonary neuroendocrine cells sense succinate to stimulate myoepithelial cell contraction
22. pH modulates the activity and synergism of the airway surface liquid antimicrobials β-defensin-3 and LL-37
23. Impaired mucus detachment disrupts mucociliary transport in a piglet model of cystic fibrosis
24. A Single-Cell Atlas of Large and Small Airways at Birth in a Porcine Model of Cystic Fibrosis
25. Anion Transport Across Human Gallbladder Organoids and Monolayers
26. Sa1172: PANCREATIC ENZYME TREATMENT OF OBSTRUCTIVE MECONIUM FROM CYSTIC FIBROSIS PIGS
27. Genotype-specific alterations in vascular smooth muscle cell function in cystic fibrosis piglets
28. Delayed neutrophil apoptosis enhances NET formation in cystic fibrosis
29. Assessing mucociliary transport of single particles in vivo shows variable speed and preference for the ventral trachea in newborn pigs
30. Cystic Fibrosis Transmembrane Conductance Regulator Potentiation as a Therapeutic Strategy for Pulmonary Edema: A Proof-of-Concept Study in Pigs
31. Acidic pH increases airway surface liquid viscosity in cystic fibrosis
32. Measurement of Mucociliary Transport: Novel Application of Positron Emission Tomography
33. Elastic mucus strands impair mucociliary clearance in cystic fibrosis pigs
34. The Rapid Reduction of Infection-Related Visits and Antibiotic Use Among People With Cystic Fibrosis After Starting Elexacaftor-Tezacaftor-Ivacaftor
35. CFTR-deficient pigs display peripheral nervous system defects at birth
36. Computer-aided analysis of airway trees in micro-CT scans of ex vivo porcine lung tissue
37. Pancreatic Damage in Fetal and Newborn Cystic Fibrosis Pigs Involves the Activation of Inflammatory and Remodeling Pathways
38. Cellular and molecular architecture of submucosal glands in wild-type and cystic fibrosis pigs
39. Combining Ivacaftor and Intensive Antibiotics Achieves Limited Clearance of Cystic Fibrosis Infections
40. Pigs and humans with cystic fibrosis have reduced insulin-like growth factor 1 (IGF1) levels at birth
41. Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs
42. Cystic Fibrosis Transmembrane Conductance Regulator Intracellular Processing, Trafficking, and Opportunities for Mutation-Specific Treatment
43. Effects of Tham Nasal Alkalinization on Airway Microbial Communities: A Pilot Study in Non-CF and CF Adults
44. Early Lung Disease Exhibits Bacteria-Dependent and -Independent Abnormalities in Cystic Fibrosis Pigs
45. Inflammatory cytokines TNF-α and IL-17 enhance the efficacy of cystic fibrosis transmembrane conductance regulator modulators
46. V-Type ATPase Mediates Airway Surface Liquid Acidification in Pig Small Airway Epithelial Cells
47. Early Airway Structural Changes in Cystic Fibrosis Pigs as a Determinant of Particle Distribution and Deposition
48. Cystic Fibrosis Transmembrane Conductance Regulator in Sarcoplasmic Reticulum of Airway Smooth Muscle. Implications for Airway Contractility
49. CYSTIC FIBROSIS: Airway acidification initiates host defense abnormalities in cystic fibrosis mice
50. Rapid Reduction of Infection-Related Visits and Antibiotic Use Among People With Cystic Fibrosis After Starting Elexacaftor-Tezacaftor-Ivacaftor.
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