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Williams‐Campbell syndrome complicated with pulmonary hypertension and Type 2 respiratory failure: An adult case report.

Authors :
Liu, Meng
Yuan, Qing
Zhao, Haimeng
Wang, Yuguang
Source :
Clinical Respiratory Journal. Dec2019, Vol. 13 Issue 12, p795-799. 5p.
Publication Year :
2019

Abstract

Williams‐Campbell syndrome, is a rare disorder characterized by a deficiency of cartilage in subsegmental bronchi, leading to distal airway collapse and bronchiectasis, which typically affects the fourth‐ to sixth‐order bronchi. This article reported a 31‐year‐old female patient who was diagnosed with Williams‐Campbell syndrome with pulmonary hypertension and Type 2 respiratory failure due to extensive cystic bronchiectasis. CT of the thorax showed the affected bronchi had characteristic ballooning on inspiration and collapse on expiration. [ABSTRACT FROM AUTHOR]

Details

Language :
English
ISSN :
17526981
Volume :
13
Issue :
12
Database :
Academic Search Index
Journal :
Clinical Respiratory Journal
Publication Type :
Academic Journal
Accession number :
139960279
Full Text :
https://doi.org/10.1111/crj.13090