腹膜后巨大淋巴管瘤1例报告及文献复习.

Objective: To analyze the clinical manifestation, imaging feature, treatment option and postoperative standardized management of the patient with retroperitoneal giant lymphangioma, and to improve the clinicians’ understanding of this disease. Methods: The clinical data of one patient with retroperitoneal giant lymphangioma were collected.The patients was diagnosed according to the patient’s specialist examination and imaging characteristics, and the selection of treatment measures and postoperative standardized management were analyzed. Results: The patient, a 33-year-old woman, was admitted to the hospital due to “abdominal distension for 2 months”. The specialist examination results showed the abdomen was slightly swelling, without other obvious abnormalities； the full abdominal percussion was mainly voiced, and the abdominal percussion changed into dulled drums at the midaxillary line, the mobile dullness was negative, the bowel sound was normal, and there were no water sound. There was a lump with the size of 17 cm×9 cm×26 cm which was soft, unclear boundary, inactive, feminine, negative for tenderness, the auscultation did not semell and vascular murmurs. The gynecological color ultrasound results showed that a large anedomic area was detected above the uterus reaching up to the lower part of the process, with a width of 18.6 cm, irregular morphology and with separations inside. The computed tomography（CT） results of the abdomen showed that the left renal pelvis and the upper segment of ureter expended, and the watery density opacity could be seen inside. The massive cystic mass can be seen in the abdominal cavity, about 17.9 cm×9.0 cm×26.7 cm, the cyst nodules shadow could be seen locally, with slight enhancement on the enhanced scan, the punctate calcification could be seen locally in the focus, and the other abnormalities were not found. The intraperitoneal cystic and space occupying in the abdominal cavity was considered, excluding the compression of the left ureter, secondary expansion and hydronephrosis of the left kidney and left upper segment of ureter. The abdminal neoplasm resection was performed, and the patient was diagnosed as retroperitoneal giant lymphangiome the surgical process was still smooth, and the postoperative standardized management was performed and the patient was discharged from the hospital. Conclusion: The clinical manifestations of retroperitoneal giant lymphangioma are poor. At present, the most valuable imaging diagonsis method of retroperitoneal giant lymphangioma is CT and magnetic resonance imaging （MRI), and surgical treatment is the preferred treatment measure. [ABSTRACT FROM AUTHOR]