Jadassohn–Dössekker's atypical tuberous myxedema: Report of three cases and review of literature.

Atypical tuberous myxedema (ATM) is a rare skin condition first described by Jadassohn and Dössekker in 1916.[1] Belonging to the heterogeneous group of mucinoses, ATM is considered as an atypical presentation of scleromyxedema with diffuse nodular thickening of the skin and without monoclonal gammopathy. A biopsy sample from a nodule revealed diffuse dermal mucin deposits, extensive fibrosis and fibroblastic proliferation. A deep incisional biopsy sample of the neck revealed diffuse deposit of mucin associated with an extensive fibrosis and a fibroblastic proliferation. [Extracted from the article]