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Extranodal Rosai-Dorfman Disease: a rare presentation involving anterior chest wall in a middle-aged female.

Authors :
Agarwal, Abhimanyu
Ravindran, Aishwarya
Donahue, James
Eltoum, Isam-Eldin
Abozeed, Mostafa
Source :
Skeletal Radiology. Mar2024, Vol. 53 Issue 3, p589-594. 6p.
Publication Year :
2024

Abstract

Rosai-Dorfman Disease is a rare benign disorder involving overproduction of immune cells, causing swollen lymph nodes and, in rare cases, the sternum. The sternal involvement may cause chest pain and masses. Diagnosis is confirmed through clinical examination, biopsy, and imaging. Treatment options may include surgery, radiation, or steroids. In this case study, we present an unusual example of extranodal Rosai-Dorfman Disease involving the sternum, bilateral clavicles and first three ribs, and pectoral muscle with no associated lymphadenopathy or systemic symptoms in a 57-year-old female. The etiology, pathology, immunohistochemistry, imaging findings, and treatment options of this unique disease are discussed. [ABSTRACT FROM AUTHOR]

Details

Language :
English
ISSN :
03642348
Volume :
53
Issue :
3
Database :
Academic Search Index
Journal :
Skeletal Radiology
Publication Type :
Academic Journal
Accession number :
174688486
Full Text :
https://doi.org/10.1007/s00256-023-04427-z