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Management of acute metabolic decompensation in maple syrup urine disease: A multi-center study.

Authors :
Yoshino, Makoto
Aoki, Kikumaro
Akeda, Hideki
Hashimoto, Kazuko
Ikeda, Tetsuo
Inoue, Fumio
Ito, Michinori
Kawamura, Masahiko
Kohno, Yoshinori
Koga, Yashutoshi
Kuroda, Yasuhiro
Maesaka, Hatae
Murakami-Soda, Hiroko
Sugiyama, Naruji
Suzuki, Yasuyuki
Yano, Shoji
Yoshioka, Akira
Source :
Pediatrics International. Apr99, Vol. 41 Issue 2, p132. 6p.
Publication Year :
1999

Abstract

Examines the management of acute metabolic decompensation in maple syrup urine disease (MSUD). Clinical phenotypes of MSUD; Therapeutic measures employed toward metabolic decompensation; Number of patients in the study who developed episodes of ketoacidosis during the neonatal period.

Details

Language :
English
ISSN :
13288067
Volume :
41
Issue :
2
Database :
Academic Search Index
Journal :
Pediatrics International
Publication Type :
Academic Journal
Accession number :
6562745
Full Text :
https://doi.org/10.1046/j.1442-200x.1999.4121044.x