Spiral Hypertrophic Cardiomyopathy as Detected by Cardiac Magnetic Resonance.

Hypertrophic cardiomyopathy (HCM) is a genetically determined heart muscle disease; characterized by left ventricular hypertrophy. Spiral HCM is described as having a counterclockwise rotation pattern of hypertrophy along with variable degrees of fibrosis. A 34-year-old female presented with symptoms suggestive of heart failure. Echocardiography showed concentric left ventricular hypertrophy with normal contractility. Cardiac MRI showed asymmetric septal hypertrophy with mid-cavity obliteration and a spiral pattern of variably increasing wall thickness. Late gadolinium enhancement demonstrated several areas of abnormal post-gadolinium uptake. We report a case of spiral HCM. We should consider cardiovascular magnetic resonance as the reference standard for diagnosing HCM. [ABSTRACT FROM AUTHOR]